DIFFICULTIES AND TREATMENT OUTCOMES OF ORTHODONTIC THERAPY OF A PATIENT WITH WILLIAMS SYNDROME

Year 2018, Volume: 5 Issue: 2, 157 - 163, 01.08.2018

Elif Dilara Şeker Türker Yücesoy Ahmet Yağcı

https://doi.org/10.15311/selcukdentj.337302

Abstract

Williams Syndrome (WS) is a rare
congenital and progressive multisystem disorder which is described with
specific systemic disorders, skeletal and dental abnormalities and tongue
thrusting. A 13-year-old patient applied to our clinic with complaining dental
caries, malocclusion and tongue thrusting. The patient was treated with a full fixed standard
edgewise appliance named as Mini Master Series from American Orthodontics
(Central Islip, N.Y., USA), 0.018
inch bracket slots) for
2 years and 8 months.

Despite poor oral hygiene, frequent
appointments helped to complete the orthodontic treatment of the patient
without caries formation. Also extraction of first molars with uncertain
prognosis provided social benefits when it was compared to healthy premolar
extractions. This case report presents the successful results of the
orthodontic therapy and difficulties of an orthodontic treatment of a patient
who was diagnosed with WS.

Keywords

Anterior Cross-bite, Chromosome Deletion, Orthodontic Treatment

WILLIAMS SENDROMLU HASTANIN ORTODONTİK TEDAVİSİNİN SONUÇLARI VE TEDAVİDEKİ ZORLUKLAR

Abstract

Williams
Syndrome (WS) nadir görülen ve progresif bir şekilde ilerleyen multi-sistem bir
sendrom olup özel sistemik hastalıklarla beraber, iskeletsel ve dental
anomalilere ek olarak dil itme durumunun izlenebildiği bir hastalık tipidir. Bu
vaka raporunda kliniğimize malokluzyon ve dil itme şikayetiyle başvuran WS
sendromlu hastanın tedavisi sırasında karşılaşılan zorluklar ve tedavi
planlaması anlatılmaktadır. Hasta standart edgewise braketler(Mini Master
Series from American Orthodontics (Central Islip, N.Y., USA),0.018 inch braket slot) ile yaklaşık
2 yıl 8 ay tedavi edilmiştir.
Bu vaka raporunda, WS tanısı ile takip edilen hastanın ortodontik tedavisi
süresince karşılaşılan zorluklar ve bunlara rağmen elde edilen başarılı
sonuçların paylaşılması hedeflenmiştir. Hastanın ortodontik tedavisi kötü oral
hijyenine rağmen sık randevu aralıkları sayesinde çürük kaviteleri oluşmadan
tamamlanmıştır. Ayrıca
hastanın sağlıklı premolar dişlerinin ağızda tutularak prognozu belirsiz molar
dişlerinin çekimi sosyal olarak hastaya avantaj sağlamıştır.

Keywords

Anterior Çapraz Kapanış, Kromozom Delesyonu, Ortodontik Tedavi

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