Diş Hekiminin Erken Teşhisi ile Gardner Sendromu: 3 Vaka Raporu

Year 2025, Volume: 12 Issue: 1, 129 - 132, 21.04.2025

Sümeyye Çelik , Alican Kuran , Umut Seki , Hasan Yılmaz , Enver Alper Sinanoğlu

https://doi.org/10.15311/selcukdentj.1492900

Abstract

Özet
Gardner sendromu otozomal dominant kalıtımlı nadir görülen bir sendromdur. Gastrointestinal poliplerin dışında ekstraintestinal bulgu olarak çenelerde osteomlar, gömülü/süpernumere dişler, epidermoid kistler, desmoid tümörler, retinal lezyonlar görülebilir. Rutin diş hekimi muayenesi esnasında panoramik radyografi ile çenelerde ekstraintestinal bulgular tespit edilebilir ve bu durum da diş hekimlerini daha ileri klinik araştırmalar yapmaya yönlendirebilecek önemli bir gösterge olabilir. Bu çalışmanın amacı kliniğimize başvurmuş ve daha önceden bu durumun farkında olmayan Gardner Sendromlu üç olguyu bildirmek ve sendromun çenelerde gözükebilecek ekstraintestinal bulguları sebebiyle diş hekimlerin dikkatini bu konuya çekmektir.

Keywords

Gardner sendromu, Osteom, Panoramik Radyografi

GARDNER SYNDROME WITH EARLY DIAGNOSIS BY THE DENTIST: 3 CASE REPORT

Abstract

Abstract
Gardner syndrome is a rare autosomal dominant inherited syndrome that may present with a number of extraintestinal findings. These include osteomas, impacted/supernumerated teeth, epidermoid cysts, desmoid tumours and retinal lesions. The presence of these extraintestinal findings in the jaws can be identified through the use of panoramic radiographs during routine dental examinations. This may serve as an important indicator that may direct dentists to further clinical investigations. The objective of this study is to present three cases of Gardner's Syndrome that were initially unaware of their condition and to highlight the importance of dentists being aware of the extraintestinal findings of the syndrome, which may appear in the jaws.

Keywords

Gardner Syndrome, Osteoma, Panoramic Radiography

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