A Rare Malignant Soft Tissue Tumor; Low Grade Fibromyxoid Sarcoma: A Case Report

Abstract

Low grade fibromyxoid sarcoma (LGFS) is a rare tumor that has a tendency to develop in deep soft tissues. Despite its histologically benign appearance it may have an aggressive clinical course with local recurrences and metastasis. It was first described by Evans in 1987. It is more often seen in young adults and especially in male patients. The tumor has a tendency to develop in deep soft tissues and less frequently in the subcutaneous tissues; the most common locations are gluteal region, chest wall, shoulder and lower extremities but rarely it may also occur in the head, cheek, jaw and the retroperitoneal area. In this case report we aimed to determine the diagnosis pathways and treatment modalities of LGFS, with regard to the literature.

Keywords

• Fibromyxoid sarcoma, soft tissue tumor, treatment

Nadir Bir Malign Yumuşak Doku Tümörü; Düşük Dereceli Fibromiksoid Sarkom: Olgu Sunumu

Abstract

Düşük dereceli fibromiksoid sarkom (DDFS) derin yumuşak dokularda gelişmeye eğilimli, histolojik olarak benign görünümüne rağmen lokal nüks ve metastaz ile agresif klinik gidiş gösterebilen nadir bir tümördür. İlk kez 1987' de Evans tarafından tanımlanmıştır. Özellikle genç erişkinlerde ve erkeklerde daha sık görülmektedir. Tümör, derin yumuşak dokularda ve daha az sıklıkla da subkutan dokularda yerleşmeye eğilimli olup en sık görülen yerler gluteal bölge, göğüs duvarı, omuz ve alt ekstremiteler olmakla birlikte nadiren baş ve retroperitoneal bölgede de ortaya çıkabilir. Bu olgu sunumunda DDFS'un tanı ve tedavisinin literatür eşliğinde irdelenmesi amaçlandı.

Keywords

• Fibromiksoid sarkom, yumuşak doku tümörü, tedavi

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