Our anesthesia experience of an infant with Pierre Robin Syndrome

Abstract

Anoplasty operation under general anesthesia for anal atresia was planned for a 2-day-old baby with Pierre-Robin syndrome (PRS). Baby was born on term (39 weeks, 2740 gr) by C/S with APGAR score at 1st and 5th minutes of 9 and 10, respectively. Birth weight was 2740 grams. Suckling throughout the examination of the patient developed spontaneous cyanotic spells and soft palate cleft and micrognathia were diagnosed. The patient was diagnosed as PRS and as he had anal atresia anoplasti was planned under general anesthesia. We aim to present the difficulties of airway management of the patients with PRS by this case report.

Keywords

• Pierre robin syndrome, newborn, airway management; anesthesia

Pierre Robin Sendromlu Bir Hastada Anestezi Deneyimimiz

Abstract

Pierre Robin Sendromlu (PRS) 2 günlük yenidoğanda anal atrezi nedeniyle genel anestezi altında anoplasti operasyonu planlandı. Termde (39 haftalık, 2740 gr), sezaryanla doğan bebeğin 1. ve 5. dakikada APGAR skoru sırayla 9 ve 10'du. Emme sırasında spontan morarma gelişen hastanın yapılan muayenesinde mikrognati ve yumuşak damak yarığı saptandı. PRS tanısı alan hastada aynı zamanda anal atrezi bulunduğu gözlendi ve genel anestezi altında anoplasti yapıldı. Bu olguda PRS' lu hastalarda hava yolu yönetiminde ortaya çıkabilecek güçlükleri tartışmayı amaçladık.

Keywords

• Pierre robin sendromu, yenidoğan, havayolu yönetimi; anestezi

References

1. Nicolai T. Management of the upper airway and congenital cyctic lung diseases in neonates. Semin Fetal Neonatal Med. 2009; 14(1):56–60.
2. Nargozian C. The airway in patients with craniofacial abnormalities. Paediatr Anaesth 2004; 14: 53–59.
3. Chadha I.A, Chadha A, Vakil S.D. Pierre Robin Syndrome- Obstructive airway and Anaesthetic Management. J Anaesth Clin Pharmacol. 2002; 18: 91-93.
4. Kurt A.N, Yılmaz E, Kurt A, Ocal C, Aygun D. [A Newborn Pierre Robin Syndrome Case]. Fırat Tıp Dergisi 2007;12(3): 225-226.
5. Asai T, Nagata A, Shingu K. Awake tracheal intubation through the laryngeal mask in neonates with upper airway obstruction. Paediatr Anaesth. 2008;18(1):77–80.
6. Mullick P, Talwar V, Gogia A.R. The Laryngeal Mask–An Aid For Difficult Intubation In A Child With Pierre-Robin Syndrome-A Case Report. Indian J Anaesth 2005; 49: 51-53.
7. Kokten G, Ozmen S, Fındıkcıoglu K, Gunaydın B. [Airway difficulty during anesthesia induction of a newborn with Pierre Robin syndrome (sequence)]. Gazi tıp dergisi 2008;19: 77-79.
8. Kamitani J, Toda Y, Nakatsuka H et al. General anesthesia outside the operating room in patients with Pierre-Robin syndrome. Masui 2005; 54(6):687-9.

9. 9- Sakai Y, Sagata Y, Kato M, Goh R, Koyama A. Anesthetic management for cleft palate plasty in a patient with Pierre-Robin syndrome. Masui 2004; 53: 813-5.
10. 10- Dell'Oste C, Savron F, Pelizzo G, Sarti A. Acute airway obstruction in an infant with Pierre Robin syndrome after palatoplasty. Acta Anaesthesiol Scand 2004; 48:787–9.