Congenital lobar emphysema that seen in two siblings

Year 2012, , 144 - 146, 01.09.2012

Yener Aydın Niyazi Diri Aysel Kurt Atila Türkyılmaz Atilla Eroğlu

https://doi.org/10.5505/sakaryamj.2012.21931

Abstract

Congenital lobar emphysema (CLE) is usually characterized by hyper-inflammation in one lobe. The left upper lobe (50%) and the right middle lobe (30%) are most often involved, followed by the right upper lobe. Family history and CLE relation did not mentioned in literature. In this article we present two siblings with CLE; one of them was 3 years old boy with right upper lobe CLE patient and the other one is, his 40 day old sister with right middle lobe CLE.

Keywords

Congenital lobar emphysema, sibling

İki kardeşte gözlenen konjenital lober amfizem

Abstract

Konjenital lober amfizem (KLA) genellikle bir lobda hiperinflasyonla karakterizedir. Sol üst lob (%50) ve sağ orta lob (%30) en sık etkilenmekte olup bunu sağ üst lob izlemektedir. Literatürde aile öyküsü ile KLA arasında bir ilişkiden bahsedilmemektedir. Bu makalede sağ üst lobu tutan 3 yaşında bir erkek olgu ile sağ orta lobu tutan 40 günlük kız çocuğu, iki kardeşteki KLA olgusu sunuldu.

Keywords

Konjenital lober amfizem, kardeş

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