Epileptik Nöbet ve Saldırgan Davranış İle Başvuran Hastada İdiyopatik Hipoparatiroidi ve Bilateral Bazal Ganglion Kalsifikasyonu: Fahr Sendromu

Year 2020, , 505 - 508, 15.09.2020

Erkut Etçioğlu , İhsan Sarıkaya Abdülkadir Aydın , Abdulkadir Tunç , Ahmet Yıldırım

https://doi.org/10.31832/smj.693271

Abstract

Fahr sendromu, simetrik ve bilateral intrakraniyal kalsifikasyon ile seyreden nadir bir hastalık tablosu olup psikiyatrik semptomlar, epileptik nöbetler, serebellar bulgular, ekstrapiramidal disfonksiyon ve demans gibi klinik belirtiler ile kendini gösterebilir. Hastalığın birçok farklı klinik tablosu olmasına rağmen etiyolojisi henüz net olarak bilinmemektedir. Bu yazıda epileptik nöbet ile başvuran ve psikiyatrik belirtileri olan Fahr sendromu olgusu sunmaktayız.

Fahr syndrome is a rare disease with symmetrical and bilateral intracranial calcium accumulation and may present with clinical symptoms such as psychiatric symptoms, epileptic seizures, cerebellar findings, extrapyramidal dysfunction and dementia. Although the disease has many different clinical manifestations, its etiology is not yet clear. In this article, we present a case of Fahr syndrome with psychiatric symptoms presenting with epileptic seizures.

Keywords

Fahr Sendromu, İntrakraniyal kalsifikasyon, Epilepsi

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