Abstract
Persistent Müllerian duct syndrome (PMDS) is a rare syndrome characterized by the presence of such structures of uterus, fallopian tubes and top 2/3 of the vagina in a male with normal phenotype. The syndrome is frequently seen in male form characterized by unilateral undescended testis and contralateral hernia uteri inguinalis or more rarely seen in female form characterized by Mullerian structures and bilateral undescended testes localized in ovarian position. In this paper, we report a patient with both PMDS and testicular cancer.
References
- Odi TO, Abdur-Rahman LO, Nasir AA. Persistent Mullerian duct syndrome: a case report and review of the literature. Afr J Paediatr Surg 2010;7:191-193.
- Inuganti RV, Bala GS, Kumar YK, Bharathi YK. Persistent Mullerian duct syndrome with testicular seminoma: A report of two cases. Indian J Urol 2011;27:407-409.
- Prakash N, Khurana A, Narula B. Persistent Müllerian duct syndrome. Indian J Pathol Microbiol 2009;52:546-548.
- Yuksel B, Saygun O, Hengirmen S. Persistent müllerian duct syndrome associated with irreducible inguinal hernia, bilateral cryptorchidism and testicular neoplasia: a case report. Acta Chir Belg 2006;106:119-120.
- Renu D, Rao BG, Ranganath K, Namitha. Persistent mullerian duct syndrome. Indian J Radiol Imaging 2010;20:72-74.
- Chiang CY, Tsai JW, Wang HP, Sung YZ, Chang LC. Hernia uterine inguinale and seminoma in persistent Müllerian duct syndrome. Int J Surg Pathol 2010;18:440-442.
- Brandli DW, Akbal C, Eugsster E, Hadad N, Havlik RJ, Kaefer M. Persistent Mullerian duct syndrome with bilateral abdominal testis: surgical approach and review of the literature. J Pediatr Urol, 2005;1:423-427.
- Shinmura Y, Yokoi T, Tsutsui Y. A case of clear cell adenocarcinoma of the mullerian duct in persistent mullerian duct syndrome: the first reported case. Am J Surg Pathol 2002;26:1231-1234
Abstract
Persistan Müllerian kanal sendromu (PMKS), uterus, fallop tüpleri ve vajenin üst 2/3' ü gibi yapıların normal fenotipli bir erkekte bulunması ile karakterize nadir bir sendromdur. Sendrom sıklıkla tek taraflı inmemiş testis, karşı tarafta herni uteri inguinalisin olduğu erkek formu ya da daha nadir ovaryan pozisyonda yer alan bilateral inmemiş testis ve Müllerian yapıların olduğu dişi formu şeklinde ortaya çıkar. Bu yazıda testis tümörlü PMKS'li bir hasta sunulmaktadır.
References
- Odi TO, Abdur-Rahman LO, Nasir AA. Persistent Mullerian duct syndrome: a case report and review of the literature. Afr J Paediatr Surg 2010;7:191-193.
- Inuganti RV, Bala GS, Kumar YK, Bharathi YK. Persistent Mullerian duct syndrome with testicular seminoma: A report of two cases. Indian J Urol 2011;27:407-409.
- Prakash N, Khurana A, Narula B. Persistent Müllerian duct syndrome. Indian J Pathol Microbiol 2009;52:546-548.
- Yuksel B, Saygun O, Hengirmen S. Persistent müllerian duct syndrome associated with irreducible inguinal hernia, bilateral cryptorchidism and testicular neoplasia: a case report. Acta Chir Belg 2006;106:119-120.
- Renu D, Rao BG, Ranganath K, Namitha. Persistent mullerian duct syndrome. Indian J Radiol Imaging 2010;20:72-74.
- Chiang CY, Tsai JW, Wang HP, Sung YZ, Chang LC. Hernia uterine inguinale and seminoma in persistent Müllerian duct syndrome. Int J Surg Pathol 2010;18:440-442.
- Brandli DW, Akbal C, Eugsster E, Hadad N, Havlik RJ, Kaefer M. Persistent Mullerian duct syndrome with bilateral abdominal testis: surgical approach and review of the literature. J Pediatr Urol, 2005;1:423-427.
- Shinmura Y, Yokoi T, Tsutsui Y. A case of clear cell adenocarcinoma of the mullerian duct in persistent mullerian duct syndrome: the first reported case. Am J Surg Pathol 2002;26:1231-1234
Details
| Primary Language | Turkish |
|---|---|
| Journal Section | Articles |
| Authors | |
| Publication Date | March 1, 2013 |
| Submission Date | September 7, 2015 |
| Published in Issue | Year 2013 Volume: 3 Issue: 1 |
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