Yenidoğanda Nadir Bir Solunum Sıkıntısı Nedeni: Konjenital Lober Amfizem

Abstract

Konjenital lober amfizem akciğerin bir veya daha fazla lobunda hiperekspansiyon, kalan akciğerde kompresyon, mediastenin karşı tarafa kayması ile karakterize nadir gelişimsel bir anomalidir. Yenidoğan döneminde solunum sıkıntısına yol açmakla birlikte, ender olarak semptomların ortaya çıkışı altıncı aya kadar gecikebilir. Hafif olgularda konservatif tedavi tercih edilirken, solunum sıkıntısının düzelmediği olgularda cerrahi girişim gerekmektedir. Burada yenidoğan döneminde tanısı konularak lobektomi uygulanmış bir konjenital lober amfizem olgusu tartışılmıştır.

Keywords

• Konjenital lober amfizem, Lobektomi, Solunum sıkıntısı, Yenidoğan

A Rare Cause of Respiratory Distress in the Newborn: Congenital Lobar Emphysema

Abstract

Congenital lobar emphysema (CLE) is a rare malformation of lung development caused by the hyperinflation of the lung lobe with compression of the normal lung parenchyma and contralateral displacement of the mediastinum. It may represent immediately at birth with respiratory insufficiency or have a slower onset at 6 months of life. The treatment of choice may be conservative in mild cases or surgical removal of the affected lobe may be needed in severe cases that have persistent or progressive respiratory distress. A baby diagnosed as having CLE and whose affected lobe was surgically removed at the newborn period is presented and discussed

Keywords

• Congenital lobar emphysema, Lobectomy, Respiratory distress, Newborn

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