Tetra Amelili Hastada Santral Venöz Kateter Yerleştirilmesine Bağlı Şilotoraks

Abstract

Tetra-ameli, tüm ekstremitelerin yokluğu ile karakterize nadir bir genetik bozukluktur. Hastalar akciğer enfeksiyonu veya ek anomalileri nedeni ile sık sık hastaneye yatmak zorunda kalırlar. Bu hastalarda kafatası ve boyundan periferik intravenöz girişimle veya internal juguler venden santral venöz kateter yerleştirilmesi (SVKY) ile damaryolu bulunabilir. SVKY sonrası damar ve sinir yaralanmaları, pnömotoraks, hemotoraks, kardiyak tamponad, pulmoner emboli, aritmi, sepsis ve giriş yerinde enfeksiyon gibi komplikasyonlar bildirilmiştir. Şilotoraks nadir bir komplikasyondur. SVKY gereken olgularda uygun kalınlık ve uzunlukta kateterin seçilmesi ve sağ internal juguler venin tercih edilmesi şilotoraksı azaltacaktır. Bu yazıda, tetra-amelili hastada damar yolu uygulamaları ve SVKY ile ilişkili şilotoraksın tanı ve tedavisinin tartışılması amaçlanmaktadır.

Keywords

• Ameli, Sanral venöz kateterizasyon, Şilotoraks, Total parenteral nutrisyon

Chylothorax Following Central Venous Catheterization in a Patient with Tetra-Amelia

Abstract

Tetra-amelia is a very rare genetic disorder, characterized by the complete absence of all extremities. Patients often have to be hospitalized because of pulmonary infection and associated abnormalities. In this patient group, venous access is possible by the insertion of either a peripheral intracath at the scalp/neck or a central venous catheter (CVC) at the internal jugular vein. Following central venous catheterization, many complications such as vessel and nerve injury, pneumothorax, hemothorax, cardiac tamponade, pulmonary embolism, arrhythmia, sepsis, and infection at the insertion site have been reported in the English literature. Chylothorax, a rare complication following central venous catheterization, can be decreased by preferring insertion of the CVC to the right internal jugular vein and using a flexible CVC of an appropriate length and gauge. Herein, insertion of CVC in a case with tetra-amelia and diagnosis and treatment of CVC-related chylothorax were summarized

Keywords

• Amelia, Central venous catheterization, Chylothorax, Total Parenteral Nutrition

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