Kawasaki Hastalığı

Abstract

Kawasaki hastalığı (mukokutanöz lenf nodu sendromu ) nedeni bilinmeyen ve genellikle 5 yaşın altındaki çocuklarda görülen bir sistemik vaskülit sendromudur. Çocukluk çağında Henoch-Schonlein vaskülitinden sonra en sık görülen ikinci vaskülit nedenidir. Hastalığın en önemli komplikasyonu koroner arter anevrizmasıdır. Bu nedenle erken tanı ve tedavi hastalığın iyi prognozu açısından çok önemlidir. Kawasaki hastalığının kesin tanı koydurucu kriterleri yoktur. Atipik veya inkomplet seyirli vakaların varlığı nedeniyle 5 günden uzun süren ateşli olgularda Kawasaki hastalığı akla getirilmeli ve hastalar kardiak komplikasyonlar açısından ekokardiografi ile değerlendirilmelidir. Erken tanı ve tedavinin önemini bir kez daha vurgulamak amacıyla hastanemize uzamış ateş nedeniyle refere edilen, koroner arter anevrizması gelişmesi nedeniyle Kawasaki hastalığı tanısı alan 5.5 aylık erkek hastayı sunuyoruz.

Keywords

• Kawasaki hastalığı, sütçocuğu, koroner arter anevrizması

KAWASAKI DISEASE

Abstract

Kawasaki disease (mucocutaneous lymph node syndrome) is a systemic vasculitic syndrome with unknown etiology which occurs predominantly in children younger than 5 years.It is the second common cause of vasculitis following Henoch-Schonlein vasculitis in childhood. The most important complication of the disease is coronary artery aneurysm. For that reason, early diagnosis and therapy is very important for good prognosis. Kawasaki disease has no certain diagnostic criteria. Because of atypical or incomplete cases, Kawasaki disease should be considered in any infant or young child with prolonged and unexplained fever and these patients should be evaluated by echocardiography for cardiac complications. We present a 5.5 month old boy referred to our hospital for prolonged fever, developing coronary artery aneurysm and diagnosed as Kawasaki disease to emphasize the importance of early diagnosis and therapy once more

Keywords

• Kawasaki disease, infant, coronary artery aneurysm

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