Geç Başlangıçlı Lineer Skleroderma

Year 2018, Volume: 12 Issue: 2, 153 - 155, 29.06.2018

İsmet Sevimli Perihan Öztürk , Mehmet Kamil Mülayım , Hülya Nazik

https://doi.org/10.21763/tjfmpc.432556

Cited By: 1

Abstract

En coup de sabre (yüzün lineer skleroderması), alın ve saçlı derinin frontopariyetal bölgesini tutan, morfeanın (lineer skleroderma) nadir görülen bir tipidir. Gelişiminde travma, immobilizasyon, BCG aşısı, K vitamini enjeksiyonları, giysilerin mekanik basısı gibi tetikleyiciler suçlanmıştır. En coup de sabre genellikle pediatrik popülasyonda görülür, olguların %67’si 18 yaşından önce tanı almıştır. Burada, 30 yaşında yetişkin bir hastaki en coup de sabre geç başlangıcı vurgulamak amacıyla sunulmuştur.

Keywords

En coup de sabre, lokalize skleroderma, morfea, geç başlangıç

Late Onset Linear Sclorederma

Abstract

En coup de sabre (linear scleroderma of
face) is a rare type of morphea (localized scleroderma) involving frontoparietal
area of the forehead and scalp. Many triggering factors have been blamed in the
development of morfea like trauma, immobilization, BCG vaccination, injections
of vitamin K, mechanical compression from clothing, etc. En coup de sabre
usually affects the pediatric population, with 67 % of patients diagnosed
before 18 years of age. In this article, it was reported to emphasize the late
started a case of 30 years old female.

En coup de sabre (yüzün lineer skleroderması), alın ve saçlı
derinin frontopariyetal bölgesini tutan, morfeanın (lineer skleroderma) nadir
görülen bir tipidir. Gelişiminde travma, immobilizasyon, BCG aşısı, K vitamini
enjeksiyonları, giysilerin mekanik basısı gibi tetikleyiciler suçlanmıştır. En
coup de sabre genellikle pediatrik popülasyonda görülür, olguların %67’si 18
yaşından önce tanı almıştır. Burada, 30 yaşında yetişkin bir hastaki en coup de
sabre geç başlangıcı vurgulamak amacıyla sunulmuştur.

Keywords

En coup de sabre, localized scleroderma, morphea

References

• 1. Fett N, Werth WP. Update on morphea: part I. Epidemiology,clinical presentation, and pathogenesis. J Am Acad Dermatol 2011; 64: 217-228.
• 2. Weibel L, Sampaio MC, Visentin MT, Howell KJ, Woo P, Harper JI. Evaluation of methotrexate and corticosteroids for the treatment of localized scleroderma (morphoea) in children. Br J Dermatol 2006; 155:1013-1020.
• 3. Cassidy JT, Petty RE. The systemic scleroderma and related disorders. In: Cassidy JT, Petty RE, editors. Textbook of pediatric rheumatology. Philadelphia: W. B. Saunders; 2001. p. 505-34.
• 4. Nelson A. Localized sclerodermas. In: Cassidy JT, Petty, RE, editors. Textbook of pediatric rheumatology. Philadelphia: W. B. Saunders; 2001. p. 535-44.
• 5. Uziel Y, Miller ML, Laxer RM. Scleroderma in children. Pediatr Clin North Am 1995; 42: 1171-1203.
• 6. Holland KE, Steffes B, Nocton JJ, Schwabe MJ, Jacobson RD, Drolet BA. Linear scleroderma en coup de sabre with associated neurologic abnormalities. Pediatrics 2006;117:132-136.
• 7. Tollefson MM, Witman PM. En coup de sabre morphea and Parry-Romberg syndrome: a retrospective review of 54 patients. J Am Acad Dermatol 2007; 56: 257.
• 8. Orozco-Covarrubias L, Guzmán-Meza A, Ridaura-Sanz C, Carrasco Daza D, Sosa-de-Martinez C, Ruiz-Maldonado R. Scleroderma 'en coup de sabre' and progressive facial hemiatrophy. Is it possible to differentiate them? J Eur Acad Dermatol Venereol. 2002;16(4):361-6.
• 9. Goodfield MJD, Jones SK, Veale DJ. The Connective Tissue Diseases. In: Burns T, Breathnach S, Cox N, Griffiths C. Eds. Rook’s Textbook of Dermatology. Wiley-Blackwell, U.K, 8 th. ed 2010;3:5164-5178.
• 10. Ehara M, Oono T, Yamasaki O, Matsuura H, Iwatsuki K. Generalized morphea-like lesions arising in mechanically-compressed areas by underclothes. Eur J Dermatol 2006; 16(3):307-309.
• 11. Katsumoto TR, Whitfield ML, Connolly MK. The pathogenesis Of systemic sclerosis. Annu Rev Pathol 2011; 6:509-37. doi: 10.1146/annurev-pathol-011110-130312.
• 12. Zulian F. Localized scleroderma in childhood. https://www.uptodate.com/contents/localized-scleroderma-in-childhood?sectionName=Linear%20scleroderma%20of%20the%20face&anchor=H10&source=see_link#H16
• 13. Brownell I, Soter NA, Franks Jr, AG. Familial linear scleroderma (en coup de sabre) responsive to antimalarials and narrowband ultraviolet B therapy. Dermatology Online Journal 2007; 13:11.
• 14. Vancheeswaran R, Black CM, David J,Hasson N, Harper J,Atherton D, et al. Childhood-onset scleroderma: Is it different from adult-onset disease. Arthritis Rheum 1996; 39:1041 9.
• 15. Arif T, Majid I, Ishtiyaq Haji ML. Late onset ‘en coup de sabre’ following trauma: Rare presentation of a rare disease. Our Dermatol Online 2015;6:49-51.
• 16. Çayırlı M, Açıkgöz G. Linear scleroderma ‘en coup de sabre’ and Epilepsy: A case report. J Turk Acad Dermatol 2013;7:137.