NÖROFİBROMATOZİS TİP-2 OLGUSUNDA İNTRAVENTRİKÜLER MENENJİOM

Abstract

GİRİŞ: Nörofıbromatozis (NF) tip-2 nadir görülen bir hastalıktır (1/210 000). Ventrikül içi menenjiomlar da nadir görülen tümörlerdir (%0,5-3). Nadir görülen bu iki patolojinin birlikteliği radyolojik ve klinik açıdan tartışılmıştır. OLGU: 63 y kadın hasta. Baş ağrısı , her iki kulakta 10 yıldır ilerleyici işitme kaybı şikayetleriyle başvurdu. Hastanın kranial MR tetkiki sonucunda her iki internal akustik kanal içinde milimetrik boyutlarda patolojik kontrast tutulumu (schwannom?), sol lateral ventrikül içinde, patolojik kontrast tutan yaklaşık 32x28x25 mm düzgün sınırlı kitle (menenjiom ?) tespit edildi. Nörolojik muayenesinde bilateral işitmede azalma dışında patolojik bulgu yoktu. Sol parietalde ciltaltında 1,5x1 cm fibromatöz lezyon vardı. Transkortikal insizyonla sol lateral ventriküldeki kitle total olarak boşaltıldı. Patoloji sonucu fibroblastik menenjiom olarak geldi. SONUÇ: İşitme kaybı ve baş ağrısı şikayeti ile gelen hastalarda nadirde olsa NF tip 2 ve eşlik eden ventrikül içi tümör akılda bulundurulmalıdır. Dr. İsmail İŞTEMEN, Dr. Salim ŞENTÜRK, Dr. Ömer FarukTÜRKOĞLU, Dr. Etem BEŞKONAKLI

Keywords

• Nörofıbromatozis
• tip-2
• intraventriküler
• menenjiom.

INTRAVENTRICULAR MENENGIOMA IN A NEUROFIBROMATOSIS TYPE-2 CASE

Abstract

INTRODUCTION: Neurofibromatosis (NF) type-2 is a rare disease(1/210 000). Also intraventricular menengiomas are rare too (%0,5-3). A rare combination of these two pathologies are discussed in the radiological and clinical aspect. CASE: 63 Y, female patient. She was admitted with headache and progressive hearing loss in both ears for 10 years. As a result of the patient’s cranial MRI, pathological contrast enhancements in the millimeter sizes (schwannoma?) were detected in the both of internal acoustic canal, and pathological contrast-enhancing mass with smooth margins of about 32x28x25 mm (menenjiom?) was detected in the left lateral ventricle. Neurological examination findings were normal except for bilateral decreased hearing. There was a 1,5x1 cm fibromatous lesion under the skin at the left parietal zone, ventricular mass was totally removed with transcortical incision. Histopathological result was reported as fibroblastic meningioma. RESULT: Hearing loss and headache can occur in patients with a complaint from the intraventricular tumors associated with NF type 2 and should be considered.

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