Ramsay-Hunt Syndrome with Maxillary Dermatome Involvement: A Case Report

Abstract

Herpes zoster (HZ) is caused by the reactivation of varicella zoster virus (VZV) that remains latent in the dorsal root ganglia after varicella infection. During the course of the disease, vesicular eruptions appear on skin of the innerved dermatome. Herpes zoster usually occurs in elderly patients. Thoracic dermatome is the most involved area in HZ. Trigeminal nerve is the most affected cranial nerve and ophthalmic branch of the trigeminal nerve involvement (ophtalmic zona) is twenty times more frequent in comparison with involvement of maxillary and mandibular branches. Ramsay-Hunt syndrome is a cranial polyneuropathy following VZV reactivation. The frequency of Ramsay-Hunt syndrome is defined as %1 in HZ infections. We present this interesting case because maxillary branch involvement with Ramsay-Hunt syndrome is a rare combination. Key words: Ramsay Hunt Syndrome; Herpes Zoster; Maxillary Zona Zoster.

Keywords

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Maksiller Dermatomu Tutan Bir Ramsay-Hunt Sendromu Olgusu

Öz

Herpes zoster (HZ) varisella enfeksiyonu sonrası arka kök gangliyonlarına yerleşen varisella zoster virüsünün (VZV) reaktivasyonu sonucu, latent kaldığı gangliyonun innerve ettiği dermatom bölgesinde veziküler lezyonlarla ortaya çıkar. Sıklıkla yaşamın ilerleyen dönemlerinde görülür. Zonada en sık tutulum torasik dermatomda olmaktadır. Kraniyal sinir tutulumu ise en sık olarak trigeminal sinirde olup, oftalmik dalın etkilenmesi (oftalmik zona), maksiller ve mandibuler dal tutulumuna göre yaklaşık yirmi kat daha sıktır. Ramsay-Hunt sendromu, varisella zoster virüsünün reaktivasyonuyla ortaya çıkan bir kraniyal polinöropatidir. Herpes zoster enfeksiyonları içerisindeki sıklığı %1 olarak tanımlanmıştır. Maksiller dal tutulumunun nadir olması ve beraberinde Ramsay-Hunt sendromu bulunması yönüyle enteresan bulunan hastanın sunulması uygun görülmüştür. Anahtar Kelime: Ramsay Hunt Sendromu; Herpes Zoster; Maxiller Zona Zoster.

Anahtar Kelimeler

• Ramsay Hunt Sendromu; Herpes Zoster; Maxiller Zona Zoster

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