A Rare Form of Tricohbezoar: A Case of Rapunzel Syndrome

Abstract

The Rapunzel syndrome consists of gastric trichobezoar with tail, epigastric mass and the gastrointestinal symptoms. A 12-year-old girl, underwent an operation for abdominal pain, nausea, vomiting, anemia and epigatsric mass, was presented in this study. Giant tricohobezoar with long tail was totally removed by laparotomy and single gastrotomy. Postoperative period was uneventful. A subsequent psychiatric consultation revealed trichotillomania and depression. Key words: Bezoar, Rapunzel syndrome, Trichotillomania, Trichophagia.

Keywords

• Bezoar, Rapunzel syndrome, Trichotillomania, Trichophagia.

Trikobezoarın Nadir Bir Formu: Rapunzel Sendromu Olgu Sunumu

Öz

Rapunzel sendromu, dürtüsel saç çekme ve yeme alışkanlığı nedeni ile midede oluşan trikobezoarın duodenum ve jejunuma uzanması ile birlikte karında kitle ve gastrointestinal semptomların görüldüğü nadir bir durumdur. Bu yazıda, bulantı, kusma, karın ağrısı, anemi ve epigastrik kitle nedeni ile opere edilen, 12 yaşındaki bir kız hasta sunuldu. Laparotomide, anterior gastrotomi yapılarak dev trikobezoar ve uzun kuyruğu tamamen çıkarıldı. Ameliyat sonrası dönemde sorunsuz iyileşen hastada, psikiyatrik değerlendirmede, dürtüsel saç çekme (trikotillomani) ve depresyon olduğu tespit edildi. Anahtar kelimeler: Bezoar, Rapunzel sendromu, Trikotillomania, Trikofaji.

Anahtar Kelimeler

• Bezoar, Rapunzel sendromu, Trikotillomania, Trikofaji.

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