Retrospective Review of Craniosynostosis Cases: Bursa Uludağ University Experience

Yıl 2024, , 85 - 88, 17.05.2024

Rabia Nur Balçın , Hanside Setenay Ünal , Pınar Eser Ocak , Mevlüt Özgür Taşkapılıoğlu

https://doi.org/10.32708/uutfd.1426425

Öz

Craniosynostosis is a developmental craniofacial anomaly that causes neuronal developmental problems and abnormal skull shape. In this study, the patient files of pediatric patients who were followed and treated in our clinic between January 2005 and December 2022 were retrospectively evaluated. 94 patients were included in our study. 57 (60.6%) of the patients were male and 37 (39.4%) were female. 45 (47.9%) cases were operated for scaphocephaly, 31 (33%) for trigonocephaly, and 12 (12.8%) for plagiocephaly. There were 4 (4.25%) cases of syndromic craniosynostosis. Median operative time was 95 minutes. A significant correlation was found between operation time and hospitalization time. Postoperative complications developed in 3 (3.2%) cases. Mortality was observed in the early postoperative period in 3 (3.2%) cases. Craniosynostosis, one of the main pathologies of pediatric neurosurgery, is not just a cosmetic problem; It is a pathology that needs to be treated at the right time to ensure neuronal development. It should be kept in mind that it is a serious pathology that can cause mortality and morbidity despite developing surgical techniques.

Anahtar Kelimeler

Craniosynostosis, scaphocephaly, trigonocephaly

Kraniosinostoz Olgularının Retrospektif İncelenmesi: Bursa Uludağ Üniversitesi Deneyimi

Öz

Kraniosinostoz, beyin gelişiminde bozulmaya ve anormal kafatası şekline neden olan gelişimsel bir kraniofasiyal anomalidir. Bu çalışmamızda kliniğimizde Ocak 2005- Aralık 2022 tarihleri arasında takip ve tedavi edilen pediatrik hastaların dosyaları retrospektif olarak incelenmiştir. Çalışmamıza 94 hasta dahil edilmiştir. Hastaların 57 (%60,6) tanesi erkek, 37’si (%39,4) kadındı. 45 (%47,9) olgu skafosefali, 31 (%33) olgu trigonosefali, 12 plagiosefali (%12,8) nedeni ile opere edildi. 4 (%4,25) sendromik kraniosinostoz olgusu mevcuttu. Median operasyon süresi 95 dakikaydı. Operasyon süresi ile yatış süresi arasında anlamlı korelasyon saptandı. 3 (%3,2) olguda postoperatif komplikasyon gelişti. 3 (%3.2) olguda postoperatif erken dönemde mortalite gözlendi. Pediatrik nöroşirürjinin ana patolojilerinden biri olan kraniosinositoz sadece kozmetik bir sorun değil; nöronal gelişimin sağlanması için doğru zamanda tedavi edilmesi gereken bir patolojidir. Gelişen cerrahi tekniklere rağmen mortalite ve morbiditelere neden olabilecek ciddi bir patoloji olduğu akılda tutulmalıdır.

Anahtar Kelimeler

Kraniosinositoz, skafosefali, trigonosefali

Etik Beyan

Uludağ Üniversitesi Tıp Fakültesi Klinik Araştırmalar Etik Kurulu tarafından 10 Ekim 2023 tarih ve Karar No: 2023-19/21 ile etik kurul onayı alınmıştır. Yazarların çıkar çatışması yoktur

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