Alt Gastrointestinal Kanaması Olan bir Yenidoğanda Bağırsak Lenfanjiyomatozu: Tanı Zorluğu

Abstract

Doğumsal kistik lenfatik malformasyonlar, yumuşak dokular, akciğerler, abdominal organlar ve kemiklerin lenfatik dokusunu etkileyen nadir bozukluklardır. Biz, doğum sonrası kanlı dışkı ile başvuran ve daha sonra jejunumda lenfanjiyom tanısı konan bir yenidoğan kız olguyu sunuyoruz. Olgumuzun ilginç yönü, şiddetli aktif kanamanın medikal tedavi ve kan transfüzyonu ile kontrol altına alınamaması ve bunun pediatrik cerrahi ekibi tarafından acil cerrahi müdahale gerektirmesiydi. Operasyon sırasında jejunal bağırsak segmentinde lenf sıvısı ile dolu iki kistik yapı tespit edildi ve rezeksiyon ile çıkarıldı. Doğumsal kistik intestinal lenfanjiyom tanısı, yenidoğan döneminde rektal kanama ile başvuran, yaşamı tehdit eden bir durum olarak düşünülmelidir.

Keywords

• Yenidoğan
• konjenital kistik intestinal lenfanjiom
• kanlı dışkı
• kistektomi

Intestinal Lymphangiomatosis in a Newborn with Lower Gastrointestinal Bleeding: Diagnostic Challenge

Abstract

Congenital cystic lymphatic malformations are rare disorders of the lymphatic tissue lining the soft tissues, lungs, abdominal organs, and bones. We report a case of a female neonate who presented with bloody stools and was subsequently diagnosed with a jejunal lymphangioma. An interesting aspect of our case was that the severe active hemorrhage could not be controlled with medical management and blood transfusion, necessitating urgent surgical intervention by the pediatric surgery team. During the operation, two cystic structures filled with lymphatic fluid were identified in the jejunal bowel loop and were removed by resection. The diagnosis of congenital cystic intestinal lymphangioma, a life-threatening condition presenting with rectal bleeding in the neonatal period, should be considered.

Keywords

• Newborn
• congenital cystic intestinal lymphangioma
• bloody faeces
• cystectomy

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