A rare clinical entity: Two cases of retroperitoneal fibrosis with different approach and consequences

Öz

Retroperitoneal fibrosis is a rare disease, characterized by the presence of a retroperitoneal tissue, consisting of chronic inflammation and marked fibrosis, which often entraps the ureters or other abdominal organs. Early symptoms are nonspecific as abdominal or lumbar discomfort. As the fibrosis progresses, the compressive effects determine the symptomatic evolution. Retroperitoneal fibrosis diagnosis is usually delayed, which can result in permanent organ failure and mortality. We present herein two cases of retroperitoneal fibrosis diagnosed in different stages of the disease and resulting in different outcomes. Our aim is to stress the importance of early diagnosis in preserving organ function.

Anahtar Kelimeler

• Keywords: Retroperitoneal fibrosis, renal failure, retroperitoneal mass

Nadir bir klinik durum: Farklı yaklaşım ve sonlanımlarla iki retroperitoneal fibrozis olgusu

Öz

Retroperitoneal fibroz, kronik inflamasyon ve belirgin fibroz içeren sıklıkla üreterleri ya da diğer intraabdominal organları çevreleyen retroperitoneal bir dokunun varlığı ile karakterize nadir bir hastalıktır. Erken dönem semptomları karında ve lumbar bölgede rahatsızlık şeklinde nonpesifik özelliktedir. Fibroz ilerledikçe oluşan bası etkisi septomlarda artışı belirler. Nadir bir klinik durum olması ve klinik ve fizik muayene bulgularının nonspesifik olması çoğu zaman teşhisi geciktirir ve kalıcı organ yetmezliği ve mortaliteye yol açar. Biz burada hastalığın farklı evrelerinde tanı almış ve farklı şekillerde sonuçlanmış iki retroperitoneal fibroz olgusunu sunduk. Amacımız erken teşhisin organ fonksiyonlarını korumadaki önemini vurgulamaktır.

Anahtar Kelimeler

• Retroperitoneal fibrozis, böbrek yetersizliği, retroperitoneal kütle

Kaynakça

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