Derleme

Talasemilerde Solunum Sistemi Bozuklukları

Cilt: 26 Sayı: 3 30 Eylül 2017
Tuğçe Kazgan , Betül Yağcı Küpeli
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Respiratory System Disorders in Thalasemia

Abstract

Thalassemia major is a worldwide healthcare problem requiring high cost medical treatment. Patients usually die of treatment associated complications in the second decade. However, improvements in treatment and meticulous follow-up strategies for treatment associated complications have led to an increase in expected life span of the patients. Regular transfusions cause progressive iron deposition in critical organs such as heart, liver and lungs. Iron deposition in the lungs results in respiratory dysfunction and impairment in quality of life of patients with thallassemia. Although iron deposition in respiratory system has been a known reality for many years in thallassemia, the effect of this deposition on respiratory functions has been an ongoing debate. 

Keywords

Thalassemia major,transfusion,respiratory function tests

Kaynakça

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Kaynak Göster

AMA
1.Kazgan T, Yağcı Küpeli B. Talasemilerde Solunum Sistemi Bozuklukları. aktd. 2017;26(3):352-377. doi:10.17827/aktd.303592