Turner Syndrome

Yıl 2012, Cilt: 21 Sayı: 4, 246 - 252, 01.12.2012

Ramachandran Sudarshan G. Sree Vijayabala Ks Prem Kumar

Öz

Turner syndrome is a genetic disorder that affects mostly females. Affected females have characteristic features such as short stature, premature ovarian failure, and several other features. Oral manifestations of this condition are not much discussed in the literature. But reported literature includes teeth, palate, periodontal and salivary changes. So the aim of this review is to illustrate the general manifestations, and especially the oral manifestations of Turner syndrome and evaluate their possible management.

Anahtar Kelimeler

Turner syndrome, Genetic disorder, X-chromosome, Tooth, Growth

Turner Sendromu

Öz

Turner sendromu daha çok kadınları etkileyenbir genetik bozukluktur. Etkilenen kadınların başlıca karakteristik özellikleri kısa boy, premature over yetmezliği, ve diğer bazı özelliklerdir .Literatürde bu durumun oral özellikleri çok fazla tartışılmamıştır. Bununla birlikte literatürde bu hastalarda diş, damak, periodontal ve salyada değişiklikler olabileceği bildirilmiştir. Bu gözden geçirmede, Turner sendromunun genel ve oral (ağızla ilgili) belirtilerinin vurgulanarak, bunların yönetinin değerlendirilmesi amaçlanmıştır.

Anahtar Kelimeler

Turner sendromu, genetic bozukluk, X kromozomu, Diş, Gelişim

Kaynakça

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