STURGE-WEBER SYNDROME:A CASE REPORT

Öz

Sturge–Weber Syndrome is rare, nonhereditary, congenital neurocutaneous disease. Leptomeningeal hemanjiom, generally unilateral port wine nevus distributing trigeminal nerve region, ocular abnormally (glaucoma) are some parts of this syndrome. The present paper reports oral findings of a 18 years old female patient with Sturge-Weber Syndrome. Sturge-Weber Syndrome must be taken into account by dentists because of its various oral manifestations

Anahtar Kelimeler

• Sturge Weber Syndrome,dentistry

STURGE-WEBER SENDROMU:BİR OLGU SUNUMU

Öz

Sturge-Weber Sendromu nadir görülen, herediter olmayan, konjenital gelişen, nörokutanöz bir hastalıktır. Bu hastalıkta leptomeningeal hemanjiom, trigeminal sinir bölgesine dağılmış genellikle tek taraflı Porto şarabı nevus, oküler anormali (glokom) görülür. Bu vaka raporunda 18 yaşındaki Sturge-Weber sendromlu bayan bir hastanın oral bulguları sunulmuştur. Sturge-Weber sendromu, hastanın sistemik durumunu etkileyebilecek çeşitli oral bulgular göstermesi sebebiyle diş hekimleri tarafından değerlendirilmesi gereken bir hastalıkdır.

Anahtar Kelimeler

• Sturge-Weber Sendromu,diş hekimliği

Kaynakça

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