ARNOLD-CHİARİ MALFORMASYONU

Öz

Arnold-Chiari veya kısaca Chiari malformasyonu; serebellumun tonsillerinin foramen magnum yoluyla aşağıya servikal spinal kanal içerisine hernie olması ile karaktarizedir ve malformasyona intrakranial veya ekstrakranial gelişimsel defektler eşlik edebilir. Posterior fossa ve orta beyni (serebellumun tonsilleri, pons ve medulla oblangatayı) ilgilendiren bu deformite grubu çocuk ve yetişkinlerde farklı şiddetlerde anatomik defektler ve morfolojilerine göre sınıflandırılır. Bu derleme çalışmasında, Chiary malformasyonun sınıflandırması, etyolojisi, epidemiyolojisi ve patofizyolojisi gözden geçirilmiştir. Klinik semptom ve bulgular ile ayırıcı teşhisi ve nörogörüntüleme parametreleri derlenerek, tedavi yaklaşımları literatüre dayanarak sunulmuştur.

Anahtar Kelimeler

• Arnold-Chiari
• malformasyon
• serebellum
• Foremen Magnum
• Orta beyin

Kaynakça

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