Dekompanse Kalp Yetmezliği Bulguları ile Başvuran Bir Primer Efüzyon Lenfoma Olgusu

Naciye Demirel Yıldırım; Naciye  Demirel Yıldırım; Ercan Bıçakcı; Ercan Bıçakcı; Tuğrul Elverdi; Tuğrul Elverdi; Mustafa Nuri Yenerel; Reyhan Diz Küçükkaya; Reyhan Diz Küçükkaya; Öner Doğan; Meliha Nalçacı; Meliha Nalçacı

A Case Applied With Decompensated Heart Failure Findings Diagnosed as Primary Effusion Lymphoma

Yıl 2008, Cilt: 2008 Sayı: 2, 152 - 155, 01.02.2008

Naciye Demirel Yıldırım Naciye Demirel Yıldırım Ercan Bıçakcı Ercan Bıçakcı Tuğrul Elverdi Tuğrul Elverdi Mustafa Nuri Yenerel Reyhan Diz Küçükkaya Reyhan Diz Küçükkaya Öner Doğan Meliha Nalçacı Meliha Nalçacı

Öz

Primary Effusion Lymphoma (PEL) is an infrequent subtype of Non-Hodgkin`s Lymphoma which is characterized by lymphomatous effusions in body cavities, not-associated with mass lesions. Generally PEL is reported in immunocompromised patients infected with human immunodeficiency virus (HIV) and Human Herpes Virus-8 (HHV-8). Recently HIV and HHV-8 negative cases were also reported. Here, we report a 76 year-old man with HIV and HHV-8 negative PEL successfully treated with R-COP chemotherapy protocol. Turkish Başlık: Dekompanse Kalp Yetmezliği Bulguları ile Başvuran Bir Primer Efüzyon Lenfoma Olgusu Anahtar Kelimeler: Primer efüzyon lenfoması Primer efüzyon lenfoması (PEL), vücut boşluklarının seröz zarlarda solid kitle ilişkisiz olarak gelişen ve lenfomatöz efüzyon ile kendini gösteren, nadir bir Hodgkin dışı lenfoma alt grubudur. Primer efüzyon lenfoması, özellikle HIV (Human immunodeficiency virus) ve HHV-8 (Human herpesvirus-8) ile infekte bağışıklığı baskılanmış kişilerde tanımlanmış olsa da, son yıllarda HIV veya HHV-8 infekte olmayan olgular da bildirilmektedir. Bu yazıda, 76 yaşında dekompanse kalp yetmezliği tablosu ile başvuran, HIV ve HHV-8 negatif PEL tanısı konularak R-COP protokolü ile başarıyla tedavi edilen bir olgu sunuldu.

Anahtar Kelimeler

Primary effusion lymphoma

Kaynakça

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