Localized Pulmonary Alveolar Proteinosis: Two Case Reports

Yıl 2014, Cilt: 31 Sayı: 3, 257 - 260, 01.07.2014

Seon Jeong Oh Ji Yung Choo Suk Keu Yeom Ki Yeol Lee Je-hyeong Kim

Öz

Background: Pulmonary alveolar proteinosis (PAP) is a relatively
rare disease characterized by abnormal accumulation of surfactantlike
material in the alveolar spaces. The classic radiologic findings
of PAP include bilateral, symmetric, diffuse ground-glass opacity
(GGO) or consolidation. The most common computed tomography
(CT) feature of PAP is widespread GGO with thickened interlobular
septa, the so-called crazy-paving pattern, which strongly suggests the
diagnosis.
Case Report: Here, we report the cases of two young male patients
with unusual presentations of PAP. One patient showed localized PAP in the left lower lobe on CT images and the other patient presented
with unilateral PAP involving the right lower lung field and
recurrence in the same area with the same pattern as the initial manifestation.
Conclusion: In conclusion, it is important for radiologiststo be aware
of potential atypical imaging findings of PAP in order to provide a
correct diagnosis. Along these lines, PAP can present as a solitary
nodular lesion or unilateral focal lesion, and can recur in the same
pattern and location

Anahtar Kelimeler

CT, localized, pulmonary alveolar proteinosis

Kaynakça

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