Primary spinal cord glioblastoma multiforme presenting with transverse myelitis

Yıl 2014, Cilt: 39 Sayı: 3, 606 - 610, 22.07.2014

Melikhan Çerçi Begül Yağcı-küpeli Ali İhsan Ökten Kerem Mazhar Özsoy Tamer Çelik Fulya Adamhasan Ümit Çelik Suzan Zorludemir Serhan Küpeli

https://doi.org/10.17826/cutf.91183

Öz

Primary spinal cord tumors are rarely encountered in childhood period. Ependymomas and pilocytic astrocytomas comprise the majority of spinal cord tumors in children. Spinal glioblastoma multiforme (GM) (grade IV astrocytoma) is a rare clinical entity accounting for only 1-3% of all pediatric intramedullary tumors. We report a 3- year-8- month-old male with primary spinal cord GM who presented with back pain, paraparesis, gait disturbance and loss of sphincter control and initially diagnosed as transverse myelitis.

Anahtar Kelimeler

Spinal cord tumors, glioblastoma multiforme, transverse myelitis, childhood

Transvers miyelitle gelen bir primer spinal kord glioblastoma multiforme vakası

Öz

Primer spinal kord tümörlerine çocukluk çağında nadiren rastlanır. Ependimomlar ve pilositik astrositomlar bunların başında gelir. Spinal glioblastoma multiforme pediatrik intramedüller tümörlerin %1-3'ünü oluşturan nadir bir antitedir.Bu yazıda sırt ağrısı, paraparezi, yürüme bozukluğu ve sfinkter fonksiyon kaybı ile başvuran ve başlangıçta transvers miyelit olarak değerlendirilen 3 yaş 8 aylık erkek hasta sunulmuştur. Klinisyenlere bu şekilde transvers miyelit bulgularıyla başvuran vakalarda intramedüller tümörlerin de ayırıcı tanıda akılda tutulması gerektiği önerilmiştir.

Anahtar Kelimeler

Spinal kord tümörleri, glioblastoma multiforme, transverse myelitis, çocukluk çağı

Kaynakça

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• Yazışma Adresi / Address for Correspondence: Dr. Serhan Küpeli, Çukurova University, Faculty of Medicine, Department of Pediatric Oncology, ADANA GSM: 905327616752
• Email: [e-mail] G eliş tarihi/Received on: 31.09.2013
• Kabul tarihi/Accepted on:07.11.2013