Yüzde Gelişen Malign Periferik Sinir Kılıfı Tümörü Olgusu

Yıl 2016, Cilt: 30 Sayı: 1, 31 - 33, 24.06.2016

Heval Selman Özkan Saime İrkören Hüray Karaca Canten Tataroğlu

Öz

Malign periferik sinir kılıfı tümörleri, iğsi hücreli agresif
tümörer olup, yumuşak doku sarkomlarının %10’luk kısmını oluştururlar. Yüz
tutulumu nadir olup, tümörler sıklıkla ekstremite ve gövdede görülür. 75
yaşında erkek hasta sol yanak bölgesinde hızlı büyüyen kitle şikayeti ile
kliniğimize başvurdu. Malign periferik sinir kılıfı tümörü tanısı konan hastaya
geniş eksizyon ve serbest radial ön kol flebi ile rekonstrüksiyon uygulandı.
İleri yaş hastalarda baş boyun kitlelerinin ayırıcı tanısında malign periferik
sinir kılıfı tümörleri düşünülmelidir.

Anahtar Kelimeler

Malign periferik sinir kılıfı tümörü, baş boyun kitleleri, serbest flep

Malignant Peripheral Nerve Sheath Tumour With Facial Involvement

Öz

Malignant
peripheral nerve sheath tumours are agressive, spindle cell sarcomas which
constitute 10% of all soft tissue sarcomas. Head and neck involment is rare
compared with extremity and axial involvement. 75 years old male patients
referred to our clinic with a fast growing mass located in the left malar
region. Malignant peripheral nerve sheath tumour diagnosis was established and
wide excision and reconstruction with free radial forearm flap was performed.
In elderly patients with head and neck masses malignant peripheral nerve sheath
tumours must be kept in mind in differantial diagnosis.

Anahtar Kelimeler

Malignant peripheral nerve sheath tumour, head and neck masses, free flap

Kaynakça

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