Öz
Wegener granulomatosis is a rare vasculitis in childhood and is associated with morbidity and mortality in untreated cases. We reported a 10 year-old female who presented with pulmonary renal syndrome. Laboratory investiga­tions revealed the diagnosis of Wegener granulomatosis, and immunosuppressive therapy was started. Renal bi­opsy was consistent with crescentic glomerulonephritis. The patient has been still followed-up with stage 4 chronic kidney disease.
Anahtar Kelimeler
Kaynakça
- Dedeoglu F, Sundel R.P. Vasculitis in Children. Pediatr Clin N Am 2005; 52: 547-75.
- Ozen S, Bakkaloglu A, Dusunsel R, et al. Childhood vas- culitides in Turkey: a nationwide survey. Clin Rheumatol 2007; 26:196-200.
- Valentini RP, Smoyer WE. Renal Vasculitis. In: Avner ED, Harmon WE, Niaudet P, eds. Pediatric Nephrology, 5th edn. USA, Lippincott Williams&Wilkins, 2004: 835-849.
- Papiris SA, Manali ED, Kalomenidis I, et al. Bench-to-bed- side review: Pulmonary–renal syndromes –an update for the intensivist. Crit Care 2007, 11: 213.
- Von Vigier RO, Trummler SA, Laux-End R, et al. Pulmo- nary renal syndrome in childhood: a report of twenty-one cases and a review of the literature. Pediatr Pulmonol 2000; 29:382–38.
- Vehaskari VM, Aviles DH. Acute glomerulonephritis and rapidly progressive glomerulonephritis. In: Kher KK, Schnaper HW, Makker SP (eds), Clinical Pediatric Neph- rology. Second edition. London: Informa UK Ltd; 2007. p: 145-154.
- Arslan Ş. Hemolitik Üremik Sendromlar. Türkiye Klinikleri Pediatri Özel Dergisi 2004, 2: 104-111.
- Rees L, Webb NJA, Brogan PA. Vasculitis. In: Rees L, Webb NJA, Brogan PA, eds. Paediatric Nephrology, 1th edn. New York, Oxford University Pres, 2007: 297-316.
- Ozen S, Ruperto N, Dillon MJ, et al. EULAR/PReS endorsed consensus criteria for the classification of childhood vascu- litides. Ann Rheum Dis. 2006; 65:936-41.
Öz
Wegener granülomatozu çocukluk çağında nadir görülen, tedavi edilmediğinde morbidite ve mortalite ile seyredebi­len bir vaskülittir. Başvurusunda pulmoner renal sendrom tablosunda olan 10 yaşındaki bir kız hasta sunuldu. Yapı­lan tetkikler sonucunda Wegener Granülomatozu tanısı konup immunosupresif tedavi başlandı. Böbrek biyopsisi kresentik glomerülonefrit ile uyumluydu. Hasta şu anda evre 4 kronik böbrek yetmezliği tanısı ile takip edilmek­tedir.
Anahtar Kelimeler
Kaynakça
- Dedeoglu F, Sundel R.P. Vasculitis in Children. Pediatr Clin N Am 2005; 52: 547-75.
- Ozen S, Bakkaloglu A, Dusunsel R, et al. Childhood vas- culitides in Turkey: a nationwide survey. Clin Rheumatol 2007; 26:196-200.
- Valentini RP, Smoyer WE. Renal Vasculitis. In: Avner ED, Harmon WE, Niaudet P, eds. Pediatric Nephrology, 5th edn. USA, Lippincott Williams&Wilkins, 2004: 835-849.
- Papiris SA, Manali ED, Kalomenidis I, et al. Bench-to-bed- side review: Pulmonary–renal syndromes –an update for the intensivist. Crit Care 2007, 11: 213.
- Von Vigier RO, Trummler SA, Laux-End R, et al. Pulmo- nary renal syndrome in childhood: a report of twenty-one cases and a review of the literature. Pediatr Pulmonol 2000; 29:382–38.
- Vehaskari VM, Aviles DH. Acute glomerulonephritis and rapidly progressive glomerulonephritis. In: Kher KK, Schnaper HW, Makker SP (eds), Clinical Pediatric Neph- rology. Second edition. London: Informa UK Ltd; 2007. p: 145-154.
- Arslan Ş. Hemolitik Üremik Sendromlar. Türkiye Klinikleri Pediatri Özel Dergisi 2004, 2: 104-111.
- Rees L, Webb NJA, Brogan PA. Vasculitis. In: Rees L, Webb NJA, Brogan PA, eds. Paediatric Nephrology, 1th edn. New York, Oxford University Pres, 2007: 297-316.
- Ozen S, Ruperto N, Dillon MJ, et al. EULAR/PReS endorsed consensus criteria for the classification of childhood vascu- litides. Ann Rheum Dis. 2006; 65:936-41.
Ayrıntılar
| Birincil Dil | Türkçe |
|---|---|
| Bölüm | Olgu Sunumları |
| Yazarlar | |
| Yayımlanma Tarihi | 1 Aralık 2010 |
| Gönderilme Tarihi | 2 Mart 2015 |
| Yayımlandığı Sayı | Yıl 2010 Cilt: 37 Sayı: 4 |