Öz
Functional Pulmonary Atresia (FPA) is a rare clinical condition. In the newborn period, pulmonary valve can not open completely when the pulmonary artery pressure higher than the right ventricle pressure. FPA have to be differentiated than anatomic pulmonary atresia in which ventricules are intact, because of different treatment strategies. In this article, two FPA cases were presented. They admitted to the hospital with cyanosis. One of them was determined anatomically as normal and the other one had Ebstein Anomaly.
Anahtar Kelimeler
Kaynakça
- Newfeld EA, Cole RB, Paul MH. Ebstein’s malformation of the tricuspid valve in the neonate. Functional and anatomic pulmonary outflow tract obstruction. Am J Cardiol 1967; 19(5): 727-31.
- Freedom RM, Culham G, Mose F, Olley PM, Rowe RD. Dif- ferentiation of functional and structural pulmonary atresia: Role of aortography. Am J Cardiol 1978; 41(5): 914-20.
- Yetman AT, Freedom RM, McCrindle BW. Outcome in cya- notic neonates with Ebstein’s anomaly. Am J Cardiol 1998; 81(6): 749–54.
- Tumbarello R, Adatia I, Yetman A, Boutin C, Izukawa T, Feedom RM. From functional pulmonary atresia to right ventricular restriction. Long term follow up of Uhl’s anom- aly. Int J Cardiol 1998; 67(2):161-4.
- Lee CL, Hsieh KS, Huang TC, Lin CC, Choong CS. Rec- ognition of functional pulmonary Atresia by color Doppler echocardiography. Am J Cardiol 1999; 83(6): 987-88.
- Weinhaus L, Jureidini S, Nouri S, Connors RH. Functional pulmonary atresia: Color flow recognition and treatment with extracorporea membrane oxygenation. Am Heart J 1990; 119(4): 980-2.
- Almeida-Filho OC, Schmidt A, Marin-Neto JA, Maciel BC. Functional pulmonary atresia in a newborn with normal in- tracardiac anatomy. Pediatr Cardiol 2002;23(6):647-9.
Öz
Fonksiyonel pulmoner atrezi (FPA) nadir görülen klinik bir durumdur. Yapısal olarak yenidoğan döneminde pulmoner arter basıncının sağ ventrikül basıncından yüksek olduğu bazı olgularda pulmoner kapağın tam olarak açılmamasıdır. İntakt ventriküllü anatomik pulmoner atrezilerden spesifik tedavi biçimlerinin farklı olmasından dolayı ayırt edilmelidir. Bu yazıda ciltte siyanoz ile başvurarak biri anatomik olarak normal saptanmış, diğerinde Ebstein anomalisi tanısı konulup izlenen iki FPA olgusu sunulmuştur.
Anahtar Kelimeler
Kaynakça
- Newfeld EA, Cole RB, Paul MH. Ebstein’s malformation of the tricuspid valve in the neonate. Functional and anatomic pulmonary outflow tract obstruction. Am J Cardiol 1967; 19(5): 727-31.
- Freedom RM, Culham G, Mose F, Olley PM, Rowe RD. Dif- ferentiation of functional and structural pulmonary atresia: Role of aortography. Am J Cardiol 1978; 41(5): 914-20.
- Yetman AT, Freedom RM, McCrindle BW. Outcome in cya- notic neonates with Ebstein’s anomaly. Am J Cardiol 1998; 81(6): 749–54.
- Tumbarello R, Adatia I, Yetman A, Boutin C, Izukawa T, Feedom RM. From functional pulmonary atresia to right ventricular restriction. Long term follow up of Uhl’s anom- aly. Int J Cardiol 1998; 67(2):161-4.
- Lee CL, Hsieh KS, Huang TC, Lin CC, Choong CS. Rec- ognition of functional pulmonary Atresia by color Doppler echocardiography. Am J Cardiol 1999; 83(6): 987-88.
- Weinhaus L, Jureidini S, Nouri S, Connors RH. Functional pulmonary atresia: Color flow recognition and treatment with extracorporea membrane oxygenation. Am Heart J 1990; 119(4): 980-2.
- Almeida-Filho OC, Schmidt A, Marin-Neto JA, Maciel BC. Functional pulmonary atresia in a newborn with normal in- tracardiac anatomy. Pediatr Cardiol 2002;23(6):647-9.
Ayrıntılar
| Birincil Dil | Türkçe |
|---|---|
| Bölüm | Olgu Sunumları |
| Yazarlar | |
| Yayımlanma Tarihi | 1 Aralık 2012 |
| Gönderilme Tarihi | 2 Mart 2015 |
| Yayımlandığı Sayı | Yıl 2012 Cilt: 39 Sayı: 4 |