Large congenital cystic asdenomatous malformation of the lung in a newborn

Yıl 2013, Cilt: 40 Sayı: 4, 665 - 667, 01.12.2013

İlyas Yolbaş Selvi Kelekçi Yusuf Kenan Haspolat Ali Güneş Velat Şen

https://doi.org/10.5798/diclemedj.0921.2013.04.0354

Öz

Congenital cystic adenomatous malformation (CCAM) of lung is a rare form of congenital hamartomatous lesions of the lung consisting of cysts filled with air. The general clinic presentation of CCAM is dyspnea in newborns. CCAM may mimic congenital pneumonia or respiratory distress syndrome. After the delivery, the newborn male who had low Apgar score and severe respiratory distress was intubated and admitted to neonatal intensive care unit. Patient was ventilated for 50 days and weaned from the mechanical ventilator at 50th day. Type II CCAM of the lung was diagnosed according to the chest radiographs and computed tomography scan signs. Although the surgeons suggested lobectomy considering the patient's not completely asymptomatic, family did not accept this operation due to the risk of death. The patient was discharged from the hospital until the next control.

Anahtar Kelimeler

Congenital cystic adenomatous malformation of lunch, newborn, conservative treatment

Yenidoğanda akciğerin büyük konjenital kistik adenomid malformasyonu

Öz

Akciğerin konjenital kistik adenoid malformasyonu akciğerin hava ile dolu kistlerinden oluşan bir hemartöz lezyondur. Genelde doğumdan sonra solunum sıkıntısı ile bulgu verir. Konjenital pnömoni, respiratuvar distress sendromu ile ayırıcı tanısı zordur. Doğumdan sonra şiddetli solunum sıkıntısı ve düşük Apgar olan bir erkek yenidoğan entübe edildikten sonra yenidoğan yoğun bakım ünitemize yatırıldı. Hasta 50 gün mekanik ventilatörde takip edildikten sonra 50. gün mekanik ventilatörden ayrıldı. Tip II Akciğerin konjenital kistik adenoid malformasyonu tanısı akciğer tomografisi ve akciğer grafi bulguları ile kondu. Cerrahi lobektomi önermesine rağmen hastanın tümüyle aseptomatik olmaması ve ölüm riski nedeniyle aile operasyonu kabul etmedi. Hasta kontrole gelmek üzere taburcu edildi.

Anahtar Kelimeler

Akciğerin konjenital kistik adenoid malformasyonu, yenidoğan, konservatif tedavi

Kaynakça

• Ch’in KY, Tang MY. Congenital asdenomatous malformation of one lobe of a lung with general anasarca. Arch Pathol 1949;48:221-229.
• Revillon Y, Jan D, Plattner V, et al. Congenital cystic asdeno- matous malformation of the lung: prenatal management and prognosis. J Pediatr Surg 1993;28:1009-1011.
• Bagalan P, Nahom A, Giorlandino C, et al. Cystic asdeno- matous malformation of the lung: Clinical evolution and management. Eur J Pediatr 1999;158:879-882.
• Ioachimescu OC, Mehta AC. From cystic pulmonary airway malformation, to bronchioloalveolar carcinoma and adeno- carcinoma of the lung. Eur Respir J 2005;26:1181.
• Sauvat F, Michel J, Benachi A, Edmond A, Revillon Y. Man- agement of Asymptomatic Neonatal Cystic Asdenomatous Malformations. J Pediatr Surg 2003;38:548-552.
• Stocker JT, Madewell JE, Drake RM. Congenital cystic as- denomatous malformation of the lung: Clussification and morphologic spectrum.. Hum Pathol 1977;8:155-171.
• Chen HW, Hsu WM, Lu FL, et al. Management of Con- genital Cystic Asdenomatous Malformation and Broncho- pulmonary Sequestration in Newborns. Pediatr Neonatol 2010;51:172−177.
• Parikh D, Samuel M. Congenital cystic lung lesions: Is surgical resection essential? Pediatr Pulmonol 2005;40:533- 537.
• Van Leeuwen K, Teitelbaum DH, Hirschl RB, et al. Prenatal diagnosis of congenital cystic asdenomatous malformation and its postnatal presentation, surgical indications, and nat- ural history. J Pediatr Surgery 1999;34:94-798.
• Hansen TN, Corbet A. Anomalies of the airways, medias- tinum and lung parenchyma. In: Taeusch HW, Ballard RA, Gleason CA (Eds). Avery’s Diseases of the newborn. Phila- delphia: Elsevier Saunders 2005: p. 747-749.
• Adzick NS, Harrison MR, Crombleholme TM, et al. Fetal lung lesions: management and outcome. Am J Obstet Gy- necol 1998;179:884-889.
• Dommergues M, Louis-Sylvestre C, Mandelbrot L, et al. Congenital asdenomatous malformation of the lung: When is active fetal therapy indicated? Am J Ob Gynecol 1997;177:953-958.