HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT

Cilt: 2 Sayı: 3 1 Eylül 2005
  • Mustafa Aydın
  • Sait Mesut Doğan
  • Metin Gürsürer
  • Tolga Onuk
  • Aydın Dursun
  • Fatih Cam
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HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT

Öz

This paper reports a 74 year-old-man with a hypertrophic cardiomyopathy associated with mid-ventricular obstruction and a secundum type atrial septal defect. He had been suffering from shortness of breath and occasional attacks of dizziness. Doppler echocardiography revealed the gradient in the mid-left ventricular area. A transesophageal echocardiogram confirmed the findings of transthoracic study and an ostium secundum-type atrial septal defect was documented. The present case represents a rare combination of hypertrophic cardiomyopathy associated with midventricular obstruction, and an ostium secundum type atrial septal defect in an elderly man. Key words: Hypertrophic cardiomyopathy, midventricular obstruction, atrial septal defect.

Anahtar Kelimeler

Kaynakça

  1. Braunwald E: cardiomyopathy: Continued progress. N Engl J Med 1989;320:800-2 Hypertrophic
  2. Maron BJ. Hypertrophic cardiomyopathy. Curr Propl Cardiol 1993;18:642-93
  3. Falicov RE, Resnekov L. Mid ventricular obstruction in hypertrophic obstructive cardiomyopathy. New diagnostic and therapeutic challenge. Br Heart J 1977;39(7):701-5
  4. Thierfelder L, Watkins H, MacRae C et al. Alpha-tropomyosin and cardiac troponin T mutations cause familial hypertrophic cardiomyopathy: a disease of the sarcomere. Cell 1994;77(5):701-12
  5. Coviello DA, Maron BJ, Spirito P et al. Clinical features of hypertrophic cardiomyopathy caused by mutation of a “hot spot” in the alpha-tropomyosin gene. J Am Coll Cardiol 1997;29(3):635-40
  6. Falicov RE, Resnekov L , Bharati S, Lev M. Mid-ventricular obstruction: a variant of obstructive cardiomyopathy. Am J Cardiol. 1976;37(3):432-7
  7. Wigle ED, Sasson Z, Henderson MA et al. Hypertrophic cardiomyopathy. The importance of the site and the extent of hypertrophy. A review. Prog Cardiovasc Dis 1985;28(1):1-83
  8. Forker AD, Morgan JR. Hypertrophic subaortic stenosis with ostium secundum atrial septal defect. Chest 1971;60:512-5

Ayrıntılar

Birincil Dil

İngilizce

Konular

-

Bölüm

-

Yazarlar

Mustafa Aydın Bu kişi benim

Sait Mesut Doğan Bu kişi benim

Metin Gürsürer Bu kişi benim

Tolga Onuk Bu kişi benim

Aydın Dursun Bu kişi benim

Yayımlanma Tarihi

1 Eylül 2005

Gönderilme Tarihi

27 Nisan 2015

Kabul Tarihi

-

Yayımlandığı Sayı

Yıl 2005 Cilt: 2 Sayı: 3

Kaynak Göster

APA
Aydın, M., Doğan, S. M., Gürsürer, M., Onuk, T., Dursun, A., & Cam, F. (2005). HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT. European Journal of General Medicine, 2(3), 129-131. https://izlik.org/JA78KR66TF
AMA
1.Aydın M, Doğan SM, Gürsürer M, Onuk T, Dursun A, Cam F. HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT. European Journal of General Medicine. 2005;2(3):129-131. https://izlik.org/JA78KR66TF
Chicago
Aydın, Mustafa, Sait Mesut Doğan, Metin Gürsürer, Tolga Onuk, Aydın Dursun, ve Fatih Cam. 2005. “HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT”. European Journal of General Medicine 2 (3): 129-31. https://izlik.org/JA78KR66TF.
EndNote
Aydın M, Doğan SM, Gürsürer M, Onuk T, Dursun A, Cam F (01 Eylül 2005) HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT. European Journal of General Medicine 2 3 129–131.
IEEE
[1]M. Aydın, S. M. Doğan, M. Gürsürer, T. Onuk, A. Dursun, ve F. Cam, “HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT”, European Journal of General Medicine, c. 2, sy 3, ss. 129–131, Eyl. 2005, [çevrimiçi]. Erişim adresi: https://izlik.org/JA78KR66TF
ISNAD
Aydın, Mustafa - Doğan, Sait Mesut - Gürsürer, Metin - Onuk, Tolga - Dursun, Aydın - Cam, Fatih. “HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT”. European Journal of General Medicine 2/3 (01 Eylül 2005): 129-131. https://izlik.org/JA78KR66TF.
JAMA
1.Aydın M, Doğan SM, Gürsürer M, Onuk T, Dursun A, Cam F. HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT. European Journal of General Medicine. 2005;2:129–131.
MLA
Aydın, Mustafa, vd. “HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT”. European Journal of General Medicine, c. 2, sy 3, Eylül 2005, ss. 129-31, https://izlik.org/JA78KR66TF.
Vancouver
1.Mustafa Aydın, Sait Mesut Doğan, Metin Gürsürer, Tolga Onuk, Aydın Dursun, Fatih Cam. HYPERTROPHIC CARDIOMYOPATHY WITH MIDVENTRICULAR OBSTRUCTION IN ASSOCIATION WITH OSTIUM SECUNDUM-TYPE ATRIAL SEPTAL DEFECT. European Journal of General Medicine [Internet]. 01 Eylül 2005;2(3):129-31. Erişim adresi: https://izlik.org/JA78KR66TF