Congenital cystic disorders of lung masquerading as complicated pneumonia and pneumothorax: A case series

Abstract

Abstract. Congenital cystic adenomatoid malformation and congenital lobar emphysema are rare embryonic congenital disorders of lung. We report seven such cases of congenital cystic pulmonary disorders out of which, four cases were of congenital cystic adenomatoid malformation and three cases of congenital lobar emphysema. All cases presented with recurrent or persistent pulmonary infection and pneumothorax. These cases had been masquerading as pneumonia and/ or its complication and were treated for it for a variable period of time before being diagnosed as congenital lung malformation after appropriate investigations. We discuss here these rare cases.

Key words: Congenital cystic adenomatoid malformation, congenital lobar emphysema, pneumonia, pneumothorax, congenital cystic disorders of lung

Keywords

• Congenital cystic adenomatoid malformation, congenital lobar emphysema, pneumonia, pneumothorax, congenital cystic disorders of lung

Kaynakça

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