Ailesel Akdeniz Ateşi ve Multipl Skleroz Birlikteliği: Olgu Sunumu

Yıl 2020, Cilt: 1 Sayı: 1, 22 - 25, 02.11.2020

Duygu Arslan Mehdiyev Egemen İdiman

https://doi.org/10.48176/esmj.2020.6

Öz

Ailevi Akdeniz Ateşi (FMF) etnik kökenli, tekrarlayan akut ateş ve seröz zarların iltihabı ile karakterize, otozomal resesif geçişli, genetik bir hastalıktır. Multipl skleroz (MS) multifaktöryel etyolojiye sahip santral sinir sisteminin enflamatuar demiyelinizan bir hastalığıdır. FMF seyrinde santral sinir sistemi tutulumu sık görülen bir durum değildir. FMF’in multipl skleroz ile ilişkisi olduğunu savunan görüşler yanı sıra bunun rastlantısal bir birliktelik olduğunu iddia eden görüşler de bulunmaktadır. Bu yazıda FMF tanılı bir hastada multipl skleroz tanısı koyulma süreci paylaşılmıştır.

Anahtar Kelimeler

Multipl skleroz, Ailesel Akdeniz Ateşi, MEFV, Pyrin

Coexistence of Familial Mediterranean Fever and Multiple Sclerosis: A Case Report

Öz

Familial Mediterranean Fever (FMF) is an autosomal recessively inherited genetic disease of ethnic origin, characterized by recurrent acute fever and inflammation of the serous membranes. Multiple sclerosis (MS) is an inflammatory demyelinating disease of the central nervous system with a multifactorial etiology. Central nervous system involvement is not common in the course of FMF. There are opinions arguing that FMF is related to multiple sclerosis as well as claiming that it is a coincidental association. In this article, the process of diagnosing multiple sclerosis in a patient with FMF is shared.

Anahtar Kelimeler

Multiple sclerosis, Familial Mediterranean Fever, MEFV, Pyrin

Kaynakça

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