Alternanting Hemiplegia of Childhood Associated With Bilateral Ptosis in A 3-Year-Old Girl

Yıl 2006, Cilt: 11 Sayı: 1, 81 - 82, 01.02.2006

Nimet Kabakuş Abdullah Kurt Ayşegül Neşe Çitak Kurt

Öz

Alternating hemiplegia of childhood=Alternating hemiplegia of childhood is a rare and poorly understood clinical syndrome that has hemiplegia as the major feature. The syndrome has been linked to migraine, epilepsy and familial paroxysmal choreoathetosis. Cranial nerve dysfunctions are very rare in Alternating hemiplegia of childhood. We present a child with Alternating hemiplegia of childhood who had two attacks associated with ptosis . Flunarizine therapy was started to prevent a new attack of Alternating hemiplegia of childhood and she has remained free of symptoms with no residual signs during the 18-month follow-up period. As in our case, different forms of Alternating hemiplegia of childhood may be seen and an attack including hemiplegia-ptosis may become an Alternating hemiplegia of childhood episode. ©2006, Fırat Üniversitesi, Tıp Fakültesi

Anahtar Kelimeler

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Üç Yaşında Kız Hastada Bilateral Pitosiz İle İlişkili Çocukluk Çağı Alternan Hemiplejisi

Öz

Çocukluk çağının alternan hemiplejisi; nadir görülen ve hemipleji atakları ile karakterize bir sendromdur. Bu sendrom migren, epilepsy ve ailesel koreatetoz ile ilişkili olabilir. Kranial sinir disfonksiyonu ise oldukça nadirdir. Burada sunulan hastanın, pitoz gelişen iki atağı vardı. Atakların önlenmesi için hastaya Flunarizin tedavisi başlandı ve18 aydır izlenen hastanın herhangibir şikayeti olmadı. Bu olguda olduğu gibi alternan hemiplejinin değişik formları olabilir ve hemipleji-pitoz ile atak gelişebilir. ©2006, Fırat Üniversitesi, Tıp Fakültesi

Anahtar Kelimeler

Çocukluk çağı alternan hemiplejisi, pitoz, kranyal sinir disfonksiyonu

Kaynakça

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• Kabul Tarihi: 05.09.2005