Tuberosklerozla ilişkili renal anjiomiyolipomun sebep olduğu intraperitoneal kanamayı taklit eden akut retroperitoneal hematom

Öz

Tuberous sclerosis complex (TSC) is known as a neurological and dermatological disorder, but its renal manifestations are frequent and may cause death. We report a patient with TSC who showed bilateral multiple renal angiomyolipomas. Spontaneous retroperitoneal hematoma caused by renal angiomyolipoma that mimicking intraperitoneal hemorrhage was diagnosed in her clinical follow-up. We performed right total nephrectomy for controlling hemorrhage, but she died due to poor respiratory function, in fifteenth day postoperatively.

Anahtar Kelimeler

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Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis

Öz

Tuberoskleroz kompleksi (TSC) nörolojik ve dermatolojik bir hastalık olarak bilinmekteyse de; böbrekte meydana getirdiği değişiklikler nedeniyle sıklıkla karşılaşılabilmekte ve ölüme neden olabilmektedir. Biz bilateral multipl renal anjiomiyolipomu olan tuberosklerozlu bir hastayı sunmak istedik. Renal anjiomiyolipomu olan hastada spontan retroperitoneal hematom meydana geldi ve klinik takiplerinde intraperitoneal kanamayı taklit etmesiyle tanı kondu. Hemorajiyi kontrol etmek için sağ total nefrektomi yapıldı. Ancak hasta post operatif 15. gün zayıf solunum fonksiyonları nedeniyle kaybedildi.

Anahtar Kelimeler

• Anjiomiyolipom, hemoraji, tuberoskleroz

Kaynakça

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