Mitral valve prolapsus as a rare cause of sudden cardiac death case presentation and review of literature

Öz

Mitral valve prolapsus (MVP) is common heart valve disease which is often accepted as benign. Rarely arrhythmias, mitral insufficiency and infective endocarditis can be seen in this disease. Much more rarely, MVP can lead to sudden cardiac death. We want to report and discuss that successful resuscitation of sudden cardiac death of a young male patient who had MVP. After then implantable cardiac defibrillator (ICD) was implanted to him with documented ICD defibrillation of 17 times for ventricular tachycardia/fibrillation. There was no reason for malignant arrhythmia as the cause of ICD discharge other then MVP. As a rare cause of sudden cardiac death, we aimed to discuss MVP and review sudden death risk factors in this entity.

Anahtar Kelimeler

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Ani kardiyak ölümün nadir nedeni olarak mitral kapak prolapsusu vaka sunumu ve literatür derlemesi

Öz

Mitral kapak prolapsusu (MVP) çoğunlukla iyi seyirli, en yaygın kalp kapak hastalığı olarak kabul edilmektedir. Nadir olarak bu hastalıkta ventriküler ekstrasistol, mitral yetmezlik ve infektif endokardit gibi komplikasyonlar gelişebilir. Çok daha nadir olarak da MVP ani kardiyak ölüm sebebi olabilmektedir. Olgu sunumunda genç bir erkek hastada ani kardiyak ölüm ve başarılı resusitasyon uygulanan MVP olgusunu tartışmak istedik. Daha sonra implante edilebilir kardiyak defibrilatör (ICD) yerleştirilen ve tekrarlayan ventriküler taşikardi/fibrilasyon için toplam 17 defa ICD şoklaması izlenen hastada malign aritmi nedeni olarak MVP dışında hiç bir etyolojik neden bulunmadı. Literatürde de oldukça nadir bir ani kardiyak ölüm sebebi olarak bilinen MVP’yi bu yönüyle tartışmayı ve ani ölüm risk faktörlerini gözden geçirmeyi planladık.

Anahtar Kelimeler

• Ani kardiyak ölüm, aritmi, mitral kapak prolapsusu

Kaynakça

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