Neurological Involvement in Sjögren's Syndrome: Literature Review Based on Cases

Öz

Sjögren's syndrome (SS) is a chronic autoimmune vasculitic disease involving the lacrimal and salivary glands. The central and peripheral nervous system can be affected by the ratio of 1.5-20% and 10%, in SS, respectively. In this study, clinical-neuroradiological findings and response to treantment of five female patients with SS who were affected by different parts of the central nervous system were presented in the context of current literature.

Sjögren's syndrome (SS) is a chronic autoimmune vasculitic disease involving the lacrimal and salivary glands. The central and peripheral nervous system can be affected by the ratio of 1.5-20% and 10%, in SS,  respectively.  In this study, clinical-neuroradiological findings and response to treantment of five female patients with SS who were affected by different parts of the central nervous system were presented in the context of current literature.

Anahtar Kelimeler

• Sjögren’s,vasculitis,connective tissue,pain,gabapentin

Sjögren Sendromunda Nörolojik Tutulum: Olgular Temelinde Gözden Geçirme

Öz

Sjögren sendromu (SS), gözyaşı ve tükürük bezlerini tutan kronik otoimmün vaskülitik bir hastalıktır. SS’de santral sinir sistemi %1.5-20, periferik sinir sistemi ise %10 oranında etkilenebilmektedir. Bu çalışmada santral sinir sisteminin farklı bölümlerinin etkilendiği SS tanılı beş kadın olgunun klinik -nöroradyolojik bulguları ile tedaviye yanıtları güncel literatür bilgileri eşliğinde sunulmuştur.

Sjögren sendromu (SS), gözyaşı ve tükürük bezlerini tutan kronik otoimmün vaskülitik bir hastalıktır. SS’de santral sinir sistemi %1.5-20, periferik sinir sistemi ise %10 oranında etkilenebilmektedir.  Bu çalışmada santral sinir sisteminin farklı bölümlerinin etkilendiği SS tanılı beş kadın olgunun klinik -nöroradyolojik bulguları ile tedaviye yanıtları güncel literatür bilgileri eşliğinde sunulmuştur.

Anahtar Kelimeler

• Sjögren,vaskülit,bağ dokusu,ağrı,gabapentin

Kaynakça

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