Lenfanjiomatozisin Tanısal Görüntülemesi – Resimlerle Genel Bakış

Öz

Lenfanjiomatozis; kemikler, parankimal organlar ve yumuşak dokuyu kapsayan lenf kanallarının diffüz proliferasyonu ile karakterize nadir görülen konjenital bir bozukluktur. Lenfanjiomatozis sıklıkla geç çocuklukta görülür. Birden çok kemiklerde litik lezyonlar oluşturur. Hastalığın prognozu iyi huylu durumdan ölümcül hale kadar çeşitli şekillerde rapor edilmiştir. Biz özellikle mandibula tutulumu olan lenfanjiomatozisli 14 yaşındaki bir kız klinik ve görüntüleme bulguları sunuldu.

Anahtar Kelimeler

• lenfanjiomatozis, mandibula, lenfanjiyom

Diagnostic Imaging of Lymphangiomatosis- A Pictorial Overview

Öz

Lymphangiomatosis is a rare congenital disorder, characterized by a diffuse proliferation of lymphatic channels involving bones, parenchymal organs, and soft tissue. Lymphangiomatosis frequently presents in late childhood. It produces lytic lesions in multiple bones. Prognosis of the disease has been variously reported from benign to fatal. We present the clinical and imaging features of a 14-year old girl with lymphangiomatosis and particularly involvement of mandible.

Anahtar Kelimeler

• Lymphangiomatosis, mandible, lymphangioma

Kaynakça

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9. Nishimura M, Segami N, Kaneyama K, Sato J. Systemic lymphangiomatosis of bone involving the mandible with cystic hygroma of the neck. J Oral Maxillofac Surg. 2006 Jul;64(7):115760.