Mediastinal Teratoma In A Newborn Presenting With Respiratory Distress And Superior Mediastinal Syndrome: A Case Report

Yıl 2011, Cilt: 1 Sayı: 1, 21 - 24, 01.03.2011

Fatih Turna Fatma Çakmak Çelik Ünal Bıçakcı Canan Aygün Mithat Günaydın Mehmet Kefeli Şükrü Küçüködük

Öz

Background: Medistinal teratomas compose 20% of childhood mediastinal tumors, 10% of all teratomas and it is an uncommon cause of respiratory distress in neonatal period. Method: We report a newborn with mediastinal teratoma presenting with respiratory distress and superior mediastinal syndrome. The 6x 4x 2,5 cm mass adjacent to the right upper lung was totally resected. Results: Histopathologically Grade 2 immature teratoma with an intact looking capsule, and components of immature cartilage, mesenchymal and neuroepithelial tissue was identified Chemotherapy was not administered. At the 6th month of her follow up, the AFP level was 18 ng/ml in concordance with her age. No recurrence was observed. Conclusions: Most of benign mediastinal teratomas grow slowly and do not manifest symptoms until early puberty. Chest X-ray, thorax ultrasonography, computed tomography and magnetic resonance imaging are useful in identifying the localization and association of mass with peripheral tissues. Treatment of the mediastinal teratomas in children under the age of fifteen is total surgical excision.

Anahtar Kelimeler

Newborn, respiratory distress, superior mediastinal syndrome, teratoma

Yenidoğanda Solunum Güçlüğü Ve Süperior Mediasten Sendromuna Sebep Olan Mediastinal Teratom: Olgu Sunumu

Öz

Amaç: Mediastinal teratomlar, çocukluk çağı mediastinal tümörlerinin %20'sini, tüm teratomların ise %10'unu oluştururlar ve yenidoğan döneminde solunum güçlüğünün nadir nedenlerindendir. Metod: Solunum güçlüğü ve superior mediasten sendromuna sebep olan bir yenidoğan mediastinal teratom olgusu sunduk. Sağ akciğer üst loba komşu 6x4x2,5 cm'lik kitle total olarak çıkartıldı. Bulgular: Histopatolojik değerlendirmede sağlam bir kapsülle çevrili, immature kıkırdak, mezenkim ve nöroepitel dokuları içeren, ever 2 immatür teratom izlendi. Kemoterapi verilmedi. 6. Ay kontrolünde, AFP düzeyi 18 ng/ml ölçüldü ve yaşıyla uyumluydu. Rekürans görülmedi. Sonuç: İyi huylu mediastinal teratomların çoğu yavaş büyürler ve çoğu erken puberteye kadar semptom vermezler. Direk grafi, toraks ultrasonografisi, bilgisayarlı tomografi ve manyetik rezonans, kitlenin yerinin ve çevre dokularla ilişkisinin değerlendirilmesinde yardımcıdır. 15 yaşın altındaki çocuklarda mediastinal teratomların tedavisi total cerrahi eksizyondur.

Anahtar Kelimeler

Yenidoğan, solunum güçlüğü, superior mediasten sendromu, teratom.

Kaynakça

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