Determination of Nutritional Status in Children with Cystic Fibrosis

Öz

Cystic fibrosis is a disease that affects quality of life and life span as a result of mutation in the transmembrane conductivity regulator gene. The aim of this study is to determine the nutritional status of 2–18-year-old children with cystic fibrosis.75 children with cystic fibrosis between the ages of 2-18 were included in the study. The data were obtained online with the "Sociodemographic Form", "Nutrition Evaluation Form" and "24-Hour Food Consumption Record". Dietary quality, energy intake, macro and micronutrient intakes of the participants were determined by taking a 24-hour food consumption record. IBM Statistical Package for Social Sciences Version 24 statistical program and BEBIS 8.2 program were used to analyze the data obtained through the questionnaire. In this study 32 girls and 43 boys were included. It was determined that the daily energy intake of the girls was 1368 ± 394 kcal, and the boys were 1496 ± 494 kcal. When the z-score values of the participants are examined, the z-score value according to the height is minimum -4.16, maximum 3.05; It has been determined that the z-score value for weight is minimum -3.79 and maximum 2.60. The mean z-score of the participants for height was -0.25; The mean z score according to weight was determined as -0.40. The average weight of the boys is 30 kg, and the girls are 28.4 kg. More studies are needed to determine nutritional status, new nutritional therapies, and supplemental doses in children with cystic fibrosis.

Anahtar Kelimeler

• Cystic fibrosis
• nutrition
• nutritional status

Kaynakça

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