KARTAGENER SENDROMUNDA UZUN SÜRELİ GÖĞÜS FİZYOTERAPİSİNİN ÖNEMİ (OLGU SUNUMU)

Öz

Kartagener Sendromu, otozomal resessif geçişli, dekstrokardi, sinüzit ve erken dönemde kronik üst ve alt solunum yolu enfeksiyonlarıyla, geç dönemde bronşektazi ile karakterize ender görülen bir hastalıktır. Siliyal aktivitenin bozulması nedeniyle bu hastalıkta aşırı balgam retansiyonu görülür. Hastalığın medikal tedavisi semptomatiktir. Bu çalışmada Kartagener Sendromlu bir olgu sunularak 3 yıl boyunca uygulanan göğüs fizyoterapisinin etkisi değerlendirildi. Sonuç olarak; fizyoterapi merkezine uzak ikamet etmesi nedeniyle düzensiz aralıklarla ve ancak ev programı ile takip edilen hastanın solunum fonksiyon testlerinde önemli bir gelişme olmamasına rağmen semptomlarının ve hastaneye başvuru ihtiyacının azaldığı saptandı.

Anahtar Kelimeler

• Kartagener Sendromu, Göğüs Fizyoterapisi

IMPORTANCE OF LONG TERM CHEST PHYSIOTHERAPY ON KARTAGENER SYNDROME (A CASE REPORT)

Abstract

Kartagener Syndrome is a rare ilness which is autosomal recessive pattern of inheritance, dextrocardia, sinusitis and characterized by chronic upper and lower respiratory tract infections and bronchiectasis at early and late stages respectively. Because of the degeneration of ciliary activity; in this ilness, excess musus retantion is detected. The medical treatment of the ilness is symptomatic. In this study; by present a Kartagener Syndromed case, the effect of the three yeared application of the chest physiotherapy is evaluated. As a result; In spite of having no satisfactionary improvement in the pulmonary function tests of the patient who is treated on irregular interval and only with family education and home programe. An important rate of reduction in symptoms and hospital applications has been determinated.

Keywords

• Kartagener Syndrome, Chest Physiotherapy

Kaynakça

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