PULMONER ALVEOLER MİKROLİTİYAZİS: OLGU SUNUMU

Öz

Pulmoner alveoler mikrolitiyazis (PAM) intraalveoler bölgede kalsifik granüllerin birikimiyle karekterize nadir görülen bir hastalıktır. Kırk dört yaşında kadın hasta göz kanalında tıkanıklık nedeniyle planlanan operasyon öncesi çekilen akciğer radyogramında yaygın, bilateral, alt zonlarda yaygın kalsifiye mikronodüller görülmesi üzerine tetkik için servisimize yatırıldı. Yaklaşık 5-6 yıldır eforla gelen nefes darlığı tanımladı. Karbon monoksit difüzyon kapasitesi %71 olarak ölçüldü. Toraks yüksek rezolüsyonlu bilgisayarlı tomografisi PAM ile uyumlu olan hastaya fiberoptik bronkoskopi yapıldı. Hastaya histopatolojik olarak PAM tanısı konuldu. Orbita bilgisayarlı tomografisinde sol nazolacrimal kanal distalinde 6-7 mm çapında taş yönünden şüpheli görünüm ve nazolakrimal kanal stenozu saptandı. Nadir görülmesi nedeniyle olguyu literatür bilgileri ışığında sunuyoruz.

Anahtar Kelimeler

• Pulmoner alveoler mikrolitiyazis, fiberoptik bronkoskopi

PULMONARY ALVEOLAR MICROLITHIASIS: CASE REPORT

Abstract

Pulmonary alveolar microlithiasis (PAM) is a rare disorder usually presenting with extensive intra alveolar calcium deposition. 44 year old woman with nasolacrimal duct obstruction and chest radiogram showing extensive, bilateral, bazilary calcific micronoduler lesions was admitted to hospital for investigation. She told that she had sufferred breathlessness after an effort for 5-6 years. Carbon monoxide diffusion capacity was 71%. Fiberoptic bronchoscopy was performed to the patient whose thorax high resolution computed tomography was adjusted to PAM. She was diagnosed as PAM by histopathology. In her orbital computed tomography, nasolacrimal stenosis and an opacity suspected of microlith was detected. Because it is a rare disorder, we have presented the case by the light of literature.

Keywords

• Pulmonary alveolar microlithiasis, fiberoptic bronchoscopy

Kaynakça

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