Hemangiopericytoma: A case report

Yıl 2008, Cilt: 23 Sayı: 1, 20 - 25, 01.02.2008

Ali Özcan Binatlı Erel Uluğ İlker Özhan Deniz Altınel Ümit Bayol Nurcan Özdamar

Öz

Hemangiopericytoma is an uncommon neoplasm in central nervous system (CNS). Recently, it has been named under the classification of the spesific tumors of CNS in the meningioma family as the angioblastic variant by WHO in the years of 1997 and 2000. Surgery is very important for the successful treatment of these patients. Radiotherapy (RT) is helpful in the management after the operation. Because hemangiopericytomas are extremely difficult to cure surgicaly, patients should receive postoperative RT regardless of the amount of tumor resected. Guthrie et al. emphasized particularly the importance of complete tumor removal at the first operation and subsequent RT to prolong the survival period. In our case, 54- year-old male patient with Hemangiopericytoma was operated. The tumour has been totally resected and RT has been applied after the operation as it is mentioned above. The follow- up has been occuring sufficiently in our clinic.

Anahtar Kelimeler

Middle Aged, Male, Hemangiopericytoma, Neoplasms, Vascular Tissue, Magnetic Resonance Imaging, Vimentin, Radiotherapy, Treatment Outcome

Hemanjiyoperisitoma: Olgu sunumu

Öz

Santral sinir sistemi (SSS) hemanjiyoperisitoması nadir görülür. Son zamanlarda bu tümör, SSS'nin spesifik tümörleri içine dahil edilmiştir. Dünya Sağlık Örgütü'nün 1997 ve 2000 yıllarındaki sınıflandırmasında meningiom ailesi içine ve bu ailenin içinde de anjiyoblas tik varyant içine dahil edilmiştir. En etkin tedavisi tümörün total rezeksiyonu ve sonrasında da radyoterapidir (RT). Hemanjiyoperisitomanın cerrahi kürü oldukça zor olduğu için, rezeke edilen tümör miktarına bakmaksızın hastalar ameliyat sonrası RT tedavisi almalıdırlar. Guthrie ve ark. ilk operasyonda total tümör çıkarımının ve sonrasında da RT'nin önemini, hayatta kalma süresini uzatmak açısından özellikle vurgulamışlardır. Bu yazıda sunulan 54 yaşındaki erkek hastamızda tümör total rezeke edildi ve sonrasında RT için sevki yapıldı. Hastanın takibi halen tarafımızca yapılmaktadır.

Anahtar Kelimeler

Hemanjiyoperisitoma, meningeal tümörler, radyoterapi, vimentin/analiz.

Kaynakça

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