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OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM

Yıl 2015, Cilt: 19 Sayı: 3, 173 - 176, 01.09.2015

Öz

Paratestiküler Rabdomiyosarkom İntraskrotal bölgede görülen tümörler, testis ve paratestiküler yapılardan kaynaklanabilmektedirler. Paratestiküler tümörler nadir olarak görülmektedirler 1 . Malign paratestiküler tümörlerin %46,4’ünü liposarkom, %20’sini leiomyosarkom, %13’ünü malign fibröz histiositom ve %9’unu embryonel rabdomiyosarkom oluşturmaktadır 2 . RMS Rabdomiyosarkom sıklıkla çocuk ve adolesan yaş grubunda görülür ve hastalar ağrısız skrotal kitle ile başvurur 3 . Bu çalışmada sol radikal orşiektomi sonrası saptanan ve nadir görülen paratestiküler embriyonel rabdomiyosarkom olgusu literatür eşliğinde sunulmuştur

Kaynakça

  • ) Joan C. Delto, George F. Wayne, Sofia Garces, Ana M. Medina, Alan M. Nieder: An Adult Case of Paratesticular Spindle Cell Rhabdomyosarcoma Urology Case Reports 2014;2(4) 126-8
  • ) Rodríguez D, Barrisford GW, Sanchez A, Preston MA, Kreydin EI, Olumi AF: Primary spermatic cord tumors: disease characteristics, prognostic factors, and treatment outcomes. Urol Oncol 2014, 32(52):19-25.
  • ) Radouane B, El Fenni J, Chaouir S, Amil T, Hanine A, Ben Ameur M: Rhabdomyosarcome paratesticulaire: à propos d’un cas. Journal de Radiologie 2004; (6):779–81.
  • ) Demir A, Önel FF, Türkeri L. Paratesticular pleomorphic rhabdomyosarcoma in an adult. Int Urol Nephrol 2004; 36(4):577-8.
  • ) Zaslau S, Perlmutter EP, Farivar-Mohseni H, Chang WWL, Kandzari SJ. Rhabdomyosarcoma of tunica vaginalis masquerading as hydrocele. Urology 2005; (5):1001.
  • ) Haga K, Kashiwagi A, Nagamori S, ve ark. Adult paratesticular rhabdomyosarcoma. Natr Clin Pract ;2(8):398-402. ) Kaya E, Atakan IH, Kaplan M, Bilgi S. Para testicular rhabdomyosarcoma in a 2-year-old boy. Int Urol Nephrol 2003;35(1):63-4.
  • ) Ushida H, Shintaku M, Maegawa M. Mixed tumor of paratesticular rhabdomyo sarcoma and an adenomatoid tumor in an elderly patient. Urology ;59(5):773. ) Kizer WS, Dykes TE, Brent EL, Chatham JR, Schwartz BF. Paratesticular spindle cell rhabdo myosarcoma in an adult. J Urol 2001;166 (2): 606-7.
  • ) Daneshbod Y, Monabati A, Kumar PV, Rastegar M. Paratesticular spindle cell rhabdomyosarcoma diagnosed by fine needle aspiration cytology: a case report. Acta Cytol 2005;49(3):331-4.
  • ) Mak CW, Chou CK, Su CC, Huan SK, Chang JM. Ultrasound diagnosis of paratesticular rhabdomyo sarcoma. Br J Radiol 2004;77(915):250-2.
  • ) Kirkali Z, Tuzel E, Alanyali H, Ozkal S. Locally recurrent paratesticular rhabdomyosarcoma treated with surgery and radiotherapy. Urol Int 1998; (4):264-5. )
  • Rhabdomyosarcoma and the undifferantiated sarcomas. In: Pizzo PA, Poplack DG (eds), Principles and Practice of Pediatric Oncology, Lippincott Williams & Wilkins, Philadelphia, 2002,1(2) pp. 939-72.
  • ) Horn RC Jr, Enterline HT. Rhabdomyosarcoma: a clinicopathological study and classification of 39 cases. Cancer 1958:11(1):181.
  • ) Asmar L, Gehan EA, Newton WA et al. Agreement among and within groups of pathologists in the classification of rhabdomyosarcoma and related childhood sarcomas: report of an International Study of four pathology classifications. Cancer 1994;74(9)
  • ) Qualman SJ, Caffin CM, Newton WA et al: Current practice in pediatric pathology: Intergroup Rhabdo myosarcoma Study: Update for pathologists. Pediatr Dev Pathol 1998;1(6):550-61.
  • ) Michael LR, Robert CS. Pediatric urologic oncology, genitourinary rhabdomyosarcomas. In: Wein AJ, Kavoussi LR, Novick AC, Partin AW, Peters CA (Eds): Campbell-Walsh Urology, 9th ed., Philadelphia, Elsevier Saunders, 2007; 9(7) p. 3878-85.
  • ) Wolden SL, Anderson JR, Crist WM et al. Indications for radiotherapy and chemotherapy after complete resection in rhabdomyosarcoma: A report from the IRS I and III. J Clin Oncol 1999;17(11): 75.
  • ) Goldfarb B, Khoury AE, Greenberg ML; Churchill MB, Smith CR. The role of retroperitoneal lymph adenectomy in localized paratesticular rhabdo myosarcoma. J Urol. 1994;152(2):785-7.
  • ) Backhaus BO, Kaefer M, Engum SA, Davis MM. Contralateral testiculer metastasis in paratesticular rhabdomyosarcoma. J Urol 2000; 164(5): 1709-10.
  • ) Sönmezay E, Sever N, Öztürk B, Aras B, Taşçı Aİ: Paratestiküler Rabdomiyosarkom. Medical Journal of Bakırköy, 2010;6(4):181-4.

CASE REPORT: PARATESTICULAR RHABDOMYOSARCOMA

Yıl 2015, Cilt: 19 Sayı: 3, 173 - 176, 01.09.2015

Öz

Paratesticular Rhabdomyosarcoma Intrascrotal tumors may originate from testicular or paratesticular tissue. Tumors in the paratesticular region are seen rarely 1 . Among the malignant tumors, the most common histotype is liposarcoma 46.4% , followed by leiomyosarcoma LMS 20% , malignant fibrous histiocytomas MFH 13% , and embryonal rhabdomyosarcoma 9% 2 . Rhabdomyosarcoma is frequently seen in children and adolescents. The most common symptom is painless swelling in scrotum 3 . In this paper we present a case who was diagnosed as paratesticular embryonal rhabdomyosarcoma in histological examination of radical orchiectomy material

Kaynakça

  • ) Joan C. Delto, George F. Wayne, Sofia Garces, Ana M. Medina, Alan M. Nieder: An Adult Case of Paratesticular Spindle Cell Rhabdomyosarcoma Urology Case Reports 2014;2(4) 126-8
  • ) Rodríguez D, Barrisford GW, Sanchez A, Preston MA, Kreydin EI, Olumi AF: Primary spermatic cord tumors: disease characteristics, prognostic factors, and treatment outcomes. Urol Oncol 2014, 32(52):19-25.
  • ) Radouane B, El Fenni J, Chaouir S, Amil T, Hanine A, Ben Ameur M: Rhabdomyosarcome paratesticulaire: à propos d’un cas. Journal de Radiologie 2004; (6):779–81.
  • ) Demir A, Önel FF, Türkeri L. Paratesticular pleomorphic rhabdomyosarcoma in an adult. Int Urol Nephrol 2004; 36(4):577-8.
  • ) Zaslau S, Perlmutter EP, Farivar-Mohseni H, Chang WWL, Kandzari SJ. Rhabdomyosarcoma of tunica vaginalis masquerading as hydrocele. Urology 2005; (5):1001.
  • ) Haga K, Kashiwagi A, Nagamori S, ve ark. Adult paratesticular rhabdomyosarcoma. Natr Clin Pract ;2(8):398-402. ) Kaya E, Atakan IH, Kaplan M, Bilgi S. Para testicular rhabdomyosarcoma in a 2-year-old boy. Int Urol Nephrol 2003;35(1):63-4.
  • ) Ushida H, Shintaku M, Maegawa M. Mixed tumor of paratesticular rhabdomyo sarcoma and an adenomatoid tumor in an elderly patient. Urology ;59(5):773. ) Kizer WS, Dykes TE, Brent EL, Chatham JR, Schwartz BF. Paratesticular spindle cell rhabdo myosarcoma in an adult. J Urol 2001;166 (2): 606-7.
  • ) Daneshbod Y, Monabati A, Kumar PV, Rastegar M. Paratesticular spindle cell rhabdomyosarcoma diagnosed by fine needle aspiration cytology: a case report. Acta Cytol 2005;49(3):331-4.
  • ) Mak CW, Chou CK, Su CC, Huan SK, Chang JM. Ultrasound diagnosis of paratesticular rhabdomyo sarcoma. Br J Radiol 2004;77(915):250-2.
  • ) Kirkali Z, Tuzel E, Alanyali H, Ozkal S. Locally recurrent paratesticular rhabdomyosarcoma treated with surgery and radiotherapy. Urol Int 1998; (4):264-5. )
  • Rhabdomyosarcoma and the undifferantiated sarcomas. In: Pizzo PA, Poplack DG (eds), Principles and Practice of Pediatric Oncology, Lippincott Williams & Wilkins, Philadelphia, 2002,1(2) pp. 939-72.
  • ) Horn RC Jr, Enterline HT. Rhabdomyosarcoma: a clinicopathological study and classification of 39 cases. Cancer 1958:11(1):181.
  • ) Asmar L, Gehan EA, Newton WA et al. Agreement among and within groups of pathologists in the classification of rhabdomyosarcoma and related childhood sarcomas: report of an International Study of four pathology classifications. Cancer 1994;74(9)
  • ) Qualman SJ, Caffin CM, Newton WA et al: Current practice in pediatric pathology: Intergroup Rhabdo myosarcoma Study: Update for pathologists. Pediatr Dev Pathol 1998;1(6):550-61.
  • ) Michael LR, Robert CS. Pediatric urologic oncology, genitourinary rhabdomyosarcomas. In: Wein AJ, Kavoussi LR, Novick AC, Partin AW, Peters CA (Eds): Campbell-Walsh Urology, 9th ed., Philadelphia, Elsevier Saunders, 2007; 9(7) p. 3878-85.
  • ) Wolden SL, Anderson JR, Crist WM et al. Indications for radiotherapy and chemotherapy after complete resection in rhabdomyosarcoma: A report from the IRS I and III. J Clin Oncol 1999;17(11): 75.
  • ) Goldfarb B, Khoury AE, Greenberg ML; Churchill MB, Smith CR. The role of retroperitoneal lymph adenectomy in localized paratesticular rhabdo myosarcoma. J Urol. 1994;152(2):785-7.
  • ) Backhaus BO, Kaefer M, Engum SA, Davis MM. Contralateral testiculer metastasis in paratesticular rhabdomyosarcoma. J Urol 2000; 164(5): 1709-10.
  • ) Sönmezay E, Sever N, Öztürk B, Aras B, Taşçı Aİ: Paratestiküler Rabdomiyosarkom. Medical Journal of Bakırköy, 2010;6(4):181-4.
Toplam 19 adet kaynakça vardır.

Ayrıntılar

Birincil Dil Türkçe
Bölüm Case Report
Yazarlar

İbrahim Halil Bozkurt Bu kişi benim

Tarık Yonguç Bu kişi benim

Özgü Aydoğdu Bu kişi benim

Volkan Şen Bu kişi benim

Deniz Bolat Bu kişi benim

Hakan Postacı Bu kişi benim

Tamer Şahin Bu kişi benim

İsmail Basmacı Bu kişi benim

Yayımlanma Tarihi 1 Eylül 2015
Yayımlandığı Sayı Yıl 2015 Cilt: 19 Sayı: 3

Kaynak Göster

APA Bozkurt, İ. H., Yonguç, T., Aydoğdu, Ö., Şen, V., vd. (2015). OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM. İzmir Eğitim Ve Araştırma Hastanesi Tıp Dergisi, 19(3), 173-176.
AMA Bozkurt İH, Yonguç T, Aydoğdu Ö, Şen V, Bolat D, Postacı H, Şahin T, Basmacı İ. OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM. İzmir EAH Tıp Der. Eylül 2015;19(3):173-176.
Chicago Bozkurt, İbrahim Halil, Tarık Yonguç, Özgü Aydoğdu, Volkan Şen, Deniz Bolat, Hakan Postacı, Tamer Şahin, ve İsmail Basmacı. “OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM”. İzmir Eğitim Ve Araştırma Hastanesi Tıp Dergisi 19, sy. 3 (Eylül 2015): 173-76.
EndNote Bozkurt İH, Yonguç T, Aydoğdu Ö, Şen V, Bolat D, Postacı H, Şahin T, Basmacı İ (01 Eylül 2015) OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM. İzmir Eğitim ve Araştırma Hastanesi Tıp Dergisi 19 3 173–176.
IEEE İ. H. Bozkurt, “OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM”, İzmir EAH Tıp Der, c. 19, sy. 3, ss. 173–176, 2015.
ISNAD Bozkurt, İbrahim Halil vd. “OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM”. İzmir Eğitim ve Araştırma Hastanesi Tıp Dergisi 19/3 (Eylül 2015), 173-176.
JAMA Bozkurt İH, Yonguç T, Aydoğdu Ö, Şen V, Bolat D, Postacı H, Şahin T, Basmacı İ. OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM. İzmir EAH Tıp Der. 2015;19:173–176.
MLA Bozkurt, İbrahim Halil vd. “OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM”. İzmir Eğitim Ve Araştırma Hastanesi Tıp Dergisi, c. 19, sy. 3, 2015, ss. 173-6.
Vancouver Bozkurt İH, Yonguç T, Aydoğdu Ö, Şen V, Bolat D, Postacı H, Şahin T, Basmacı İ. OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM. İzmir EAH Tıp Der. 2015;19(3):173-6.