Anaesthesia in Poland syndrome: A case report

Abstract

Poland syndrome is a rare congenital anomaly. It includes in different anomalies such as musculo-skeletal system, heart, kidneys and lungs. This syndrome is characterized by thorax deformity most commonly. Ipsilateral hand anomalies are most important features and can be seen as syndactyly or ectrodactyly. Patients may have lung complications due to the use of muscle relaxants, which is used induction and maintenance of general anesthesia. In addition, these patients show increased risk of malignant hyperthermia during general anesthesia. Because of malignant hyperthermia risk, general anesthesia should be provided carefully. In this report, we discuss the anesthetic concerns related to the management of a 23-year-old female patient with right-sided Poland syndrome undergoing breast reconstruction surgery. J Clin Exp Invest 2014; 5 (4): 608-609

Keywords

• Poland syndrome, anesthetic management, congenital anomaly

Poland Sendromunda Anestezi : Bir vaka sunumu

Öz

Poland sendromu nadir görülen bir konjenital anomalidir. Kas iskelet sistemi, kalp, böbrek ve akciğerlerle ilgili birçok anomaliyi içerir. Bu sendrom sıklıkla göğüs deformitesi ile karakterizedir. İpsilateral el anomalileri en önemli özelliği olup sindaktili ve ektrodaktili gibi el anomalileri de beraberinde görülebilir. Hastalarda genel anestezi indüksiyonu ve idamesinde kas gevşetici kullanımına bağlı akciğer komplikasyonları gelişebilir. Ayrıca genel anestezi bu hastalarda malign hipertermi gelişme riskini arttırır. Malign hipertermi ve solunumsal komplikasyon gelişebilmesi riski nedeniyle genel anestezi dikkatli bir şekilde uygulanmalıdır. Biz Poland sendromlu, meme rekonstrüksiyon cerrahisi uygulanan 23 yaşında bayan hastanın anestezi yönetimini sunmayı amaçladık.

Anahtar Kelimeler

• Poland sendromu, anestezi yönetimi, konjenital anomali

Kaynakça

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