A rare cause of Ortner’s syndrome: giant pulmonary artery aneurysm secondary to Behçet’s disease

Abstract

Behçet’ s disease is a systemic autoimmune vasculitis of unknown etiology. It causes serious disability by affecting both arteries and veins. Hoarseness due to compression of the left recurrent laringeus nerve resulting from pathologies of the heart and intrathoracic great vessels is defined as Ortner’s syndrome. The most common cause of Ortner’s syndrome is left atrial enlargement due to mitral stenosis. Various intrathoracic pathologies may also be the reason. Beside, Ortner’s syndrome due to primary pulmonary artery aneurysm as a feature of Behçet’s disease is relatively rare. Herein, we report a case of a 78 year old female patient presenting with hoarseness and diagnosed as Ortner’s syndrome resulting from a giant pulmonary artery aneurysm secondary to Behçet’ s disease. J Clin Exp Invest 2015; 6 (1): 69-71 Key words: Ortner’ s Syndrome, Pulmonary Artery Aneurysm, Behçet’s Disease

Keywords

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Ortner sendromu’ nun nadir bir nedeni: Behçet hastalığına sekonder gelişen dev pulmoner arter anevrizması

Öz

Behçet Hastalığı nedeni bilinmeyen sistemik bir otoimmün vaskülittir. Hem arterleri hem de venleri tutarak ciddi sorunlara neden olabilir. Kalp ve intratorasik büyük damarların patolojilerine bağlı olarak sol rekürren laringeal sinirin kompresyonu sonucu gelişen ses kısıklığı Ortner Sendromu olarak ifade edilir. Ortner Sendromu’ nun en sık nedeni mitral darlığa bağlı olarak sol atriyum genişlemesidir. Çeşitli intratorasik patolojiler bu tablonun nedeni olabilir. Bununla birlikte Behçet Hastalığı sonucu gelişen pulmoner arter anevrizmasına bağlı Ortner Sendromu nispeten nadirdir. Biz burada ses kısıklığı ile başvuran ve yapılan incelemeler sonucunda Behçet Hastalığı’ na bağlı dev pulmoner arter anevrizması sonucu gelişen Ortner Sendromu olarak tanı alan 78 yaşında bir bayan hastayı sunuyoruz

Anahtar Kelimeler

• Ortner Sendromu, Pulmoner Arter Anevrizması, Behçet Hastalığı

Kaynakça

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