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Different Faces of Cathecolaminergic Polymorphic Ventricular Tachycardia on Epinephrine QT Stress Testing

Yıl 2020, Cilt: 23 Sayı: 1, 64 - 65, 01.04.2020

Öz

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited arrhythmic disorder characterized by exercise-induced ventricular arrhythmias and risk for sudden cardiac death. An exercise stress test is a standard method for diagnosis of CPVT, characterized by typical bidirectional polymorphic ventricular tachycardia. In patients who are not suitable for an exercise stress test, epinephrine stress testing (epinephrine challenge) can be used instead. There are a few reports in the literature discussing supraventricular tachycardias during exercise testing in pediatric CPVT patients. We present a 6-year-old boy who was admitted with syncopy. Epinehrine stress testing was performed according to the Ackerman protocol and revealed different types of tachycardias.

Kaynakça

  • 1. Leenhardt A, Lucet V, Denjoy I, Grau F, Ngoc DD, Coumel P. Catecholaminergic polymorphic ventricular tachycardia in children: a 7-year follow-up of 21 patients. Circulation 1995;91:1512-9.
  • 2. Priori SG, Napolitano C, Tiso N, Memmi M, Vignati G, Bloise R, et al. Mutations in the cardiac ryanodine receptor gene (hRyR2) underlie catecholaminergic polymorphic ventricular tachycardia. Circulation 2001;103:196-200.
  • 3. Zipes DP, Camm AJ, Borggrefe M, Buxton AE, Chaitman B, Fromer M, et al.: ACC/AHA/ESC 2006 guidelines for management of patients with ventricular arrhythmias and the prevention of sudden cardiac death: a report of the American College of Cardiology/American Heart Association Task Force and the European Society of Cardiology Committee for Practice Guidelines: Developed in collaboration with the European Heart Rhythm Association and the Heart Rhythm Society. Circulation 2006;114:e385-e484.
  • 4. Brugada P, Brugada J. Right bundle branch block, persistent ST segment elevation and sudden cardiac death: a distinct clinical and electrocardiographic syndrome. A multicenter report. J Am Coll Cardiol 1992;20:1391-6.
  • 5. Noda T, Takaki H, Kurita T, Suyama K, Nagaya N, Taguchi A, et al. Gene-specific response of dynamic ventricular repolarization to sympathetic stimulation in LQT1, LQT2 and LQT3 forms of congenital long QT syndrome. Eur Heart J 2002;23:975-83.
  • 6. Krahn AD, Gollob M, Yee R, Gula LJ, Skanes AC, Walker BD, et al. Diagnosis of unexplained cardiac arrest: role of adrenaline and procainamide infusion. Circulation 2005;112:2228-34.
  • 7. Krahn AD, Healey JS, Chauhan V, Birnie DH, Simpson CS, Champagne J, et al. Systematic assessment of patients with unexplained cardiac arrest: cardiac arrest survivors with preserved ejection fraction registry (CASPER). Circulation 2009;120:278-85.

Adrenalin Stres Testi Sırasında Ortaya Çıkan Katekolaminerjik Polimorfik Ventriküler Taşikardinin Farklı Yüzleri

Yıl 2020, Cilt: 23 Sayı: 1, 64 - 65, 01.04.2020

Öz

Katekolaminerjik polimorfik ventriküler taşikardi (CPVT), egzersize bağlı ventriküler aritmi ve ani kardiyak ölüm riski ile karakterize kalıtımsal bir aritmik hastalıktır. Egzersiz stres testi, tipik çift yönlü polimorfik ventriküler taşikardilerle sonuçlanan CPVT tanısında standart bir yöntemdir. Egzersiz stres testi için uygun olmayan hastalarda, adrenalin stres testi kullanılabilir. Literatürde pediatrik CPVT hastalarında egzersiz testi sırasında supraventriküler taşikardilerle ilgili az sayıda rapor vardır. Bu olgu sunumunda senkop şikayeti ile başvuran altı yaşında erkek çocuk hastada Ackerman protokolüne göre uygulanan adrenalin stres testiyle ortaya çıkan farklı taşikardi türlerini paylaştık.

Kaynakça

  • 1. Leenhardt A, Lucet V, Denjoy I, Grau F, Ngoc DD, Coumel P. Catecholaminergic polymorphic ventricular tachycardia in children: a 7-year follow-up of 21 patients. Circulation 1995;91:1512-9.
  • 2. Priori SG, Napolitano C, Tiso N, Memmi M, Vignati G, Bloise R, et al. Mutations in the cardiac ryanodine receptor gene (hRyR2) underlie catecholaminergic polymorphic ventricular tachycardia. Circulation 2001;103:196-200.
  • 3. Zipes DP, Camm AJ, Borggrefe M, Buxton AE, Chaitman B, Fromer M, et al.: ACC/AHA/ESC 2006 guidelines for management of patients with ventricular arrhythmias and the prevention of sudden cardiac death: a report of the American College of Cardiology/American Heart Association Task Force and the European Society of Cardiology Committee for Practice Guidelines: Developed in collaboration with the European Heart Rhythm Association and the Heart Rhythm Society. Circulation 2006;114:e385-e484.
  • 4. Brugada P, Brugada J. Right bundle branch block, persistent ST segment elevation and sudden cardiac death: a distinct clinical and electrocardiographic syndrome. A multicenter report. J Am Coll Cardiol 1992;20:1391-6.
  • 5. Noda T, Takaki H, Kurita T, Suyama K, Nagaya N, Taguchi A, et al. Gene-specific response of dynamic ventricular repolarization to sympathetic stimulation in LQT1, LQT2 and LQT3 forms of congenital long QT syndrome. Eur Heart J 2002;23:975-83.
  • 6. Krahn AD, Gollob M, Yee R, Gula LJ, Skanes AC, Walker BD, et al. Diagnosis of unexplained cardiac arrest: role of adrenaline and procainamide infusion. Circulation 2005;112:2228-34.
  • 7. Krahn AD, Healey JS, Chauhan V, Birnie DH, Simpson CS, Champagne J, et al. Systematic assessment of patients with unexplained cardiac arrest: cardiac arrest survivors with preserved ejection fraction registry (CASPER). Circulation 2009;120:278-85.
Toplam 7 adet kaynakça vardır.

Ayrıntılar

Birincil Dil İngilizce
Konular Klinik Tıp Bilimleri
Bölüm Olgu Sunumları
Yazarlar

Hasan Kafalı Bu kişi benim 0000-0002-6501-0416

Erkut Öztürk Bu kişi benim 0000-0002-1762-3269

Yakup Ergül Bu kişi benim 0000-0001-8814-0435

Yayımlanma Tarihi 1 Nisan 2020
Yayımlandığı Sayı Yıl 2020 Cilt: 23 Sayı: 1

Kaynak Göster

Vancouver Kafalı H, Öztürk E, Ergül Y. Different Faces of Cathecolaminergic Polymorphic Ventricular Tachycardia on Epinephrine QT Stress Testing. Koşuyolu Heart Journal. 2020;23(1):64-5.