Surgical Correction of Congenital Aortic and Pulmonary Stenosis in an Adult

Öz

Although aortic and pulmonary valve stenosis are among the most common congenital heart defects, the combination of both aortic and pulmonary valve stenosis in the same patient appears to be very uncommon. Accurate diagnosis of combined valvular stenosis is imperative prior to surgical correction otherwise surgery of only one of the lesions may result in an insufficient hemodynamic improvement. A 34-year-old man with congenital aortic and pulmonary valve stenosis underwent Nick's operation, aortic valve replacement, pulmonary valvotomy and resection of anomalous muscle of the right ventricular outflow tract. The operation was successfully performed and postoperative course was uneventful.

Anahtar Kelimeler

• Aortic valve stenosis; pulmonary valve stenosis; ventricular outflow obstruction;adult; congenital.

Erişkinde Konjenital Aort ve Pulmoner Stenozu Cerrahi Onarımı

Öz

Aort ve pulmoner kapak darlığı en sık görülen konjenital kalp anomalileri olmasına rağmen aynı hastada kombine olarak görülmesi nadir görülen bir durumdur. Mevcut lezyonların sadece birisine cerrahi uygulaması, hemodinamik düzelmenin yetersiz kalmasıyla sonuçlanabileceğinden, cerrahi onarımı öncesi kombine valvular stenozun kesin tanısının konulması zorunludur. Konjenital aort darlığı ile seyreden pulmoner stenozu olan 34 yaşında erkek hastaya Nick operasyonu, aort kapak replasmanı, pulmoner valvutomi ve sağ ventrikül çıkım yolundaki anormal kas bandı rezeksiyonu uygulandı. Ameliyat başarıyla gerçekleşmiş olup, ameliyat sonrası dönemi sorunsuz seyretti.

Anahtar Kelimeler

• Aort kapak darlığı; pulmoner kapak darlığı; ventrikül çıkım engeli; yetişkin;konjenital.

Kaynakça

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