Arrhythmogenic Right Ventricular Dysplasia Associated with Bicuspid Aortic Valve

Öz

A 22-year old boy was diagnosed arrhythmogenic right ventricular dysplasia (ARVD) with bicuspid aortic valve (BAV) after a symptomatic event of ventricular tachycardia originating from the right ventricle. Cardiac magnetic resonance imaging disclosed right ventricular enlargement, diffuse thinning of lateral wall and normal left ventricle. Echocardiography showed globally thinned, moderately enlarged right ventricle and bicuspid aortic valve. Cardiovascular malformations may be present with bicuspid aortic valve. Here we would like to report the first ARVD case with an accompanying BAV.

Anahtar Kelimeler

• Arrhythmogenic Right Ventricular Dysplasia, Bicuspid Aortic Valve.

Aritmojenik Sa¤ Ventrikül Displazisi ile Birlikte Olan Biküspit Aort Kapak

Öz

Sa¤ ventrikül kaynakl› ventriküler taflikardiye ba¤l› semptomu olan 22 yafl›nda erkek bir hastada aritmojenik sa¤ ventrikül displaziye (ASVD) efllik eden bikuspit aortik kapak (BAK) saptad›k. Kardiyak manyetik rezonans görüntülemede sa¤ ventrikül lateral duvarda yayg›n incelme ile geniflleme ve normal sol ventrikül saptand›. Ekokardiyografide ise sa¤ ventrikülde orta derece geniflleme ile global incelme ve BAK saptad›k. Bikuspit aortik kapak di- ¤er kardiyovasküler malformasyon ile birlikte bulunabilmektedir. Biz bu yaz›m›zda ilk defa ASVD'ye efllik eden BAK olgusunu bildirdik.

Anahtar Kelimeler

• Aritmojenik Sa¤ Ventrikül Displazisi, Bikuspit Aortik Kapak

Kaynakça

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