Surgical Treatment Of Pulmonary Artery Angiosarcoma Causing Severe Obstruction Of The Pulmonary Artery

Yıl 2009, Cilt: 12 Sayı: 1, 30 - 32, 01.01.2008

Mustafa Saçar Gökhan Önem Bahar Baltalarlı Fahri Adal› Ahmet Baltalarl›

Öz

Pulmonary artery sarcomas are rarely seen and frequently misdiagnosed as pulmonary thromboembolic disease due to the presence of similar clinical manifestations and radiologic findings. As making the certain diagnosis is very important in order to determine the treatment strategy, one needs close follow-up to make a definite diagnosis. However, most of the cases are diagnosed during the surgery or autopsy. We report the surgical outcome of a patient with pulmonary artery angiosarcoma causing severe obstruction of the pulmonary valve and main pulmonary artery.

Anahtar Kelimeler

Pulmonary artery sarcoma, cardiopulmonary bypass, pulmonary thromboembolism

Ciddi Pulmoner Arter Darl›¤›na Neden Olan Pulmoner Anjiosarkomun Cerrahi Tedavisi

Öz

Pulmoner arter sarkomlar› nadir görülür ve benzer klinik tabloya sahip olmalar›ndan dolay› s›kl›kla pulmoner tromboembolik hastal›k tan›s› konulur. Tedavi stratejisini belirlemek aç›s›ndan do¤ru tan›n›n konmas› çok önemlidir. Bu nedenle bu hastalar do¤ru teflhifl konulmas› için yak›n takip edilmelidir. Ancak olgular›n ço¤una cerrahi veya otopsi esnas›nda teflhis konulabilmektedir. Bu olgu sunumunda ana pulmoner arter ve pulmoner kapakta ciddi darl›¤a neden olan pumoner anjiosarkomlu birhastan›n teflhis ve cerrahi tedavisini de¤erlendirdik.

Anahtar Kelimeler

Pulmoner arter sarkomu, kardiyopumoner baypas, pulmoner emboli

Kaynakça

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• Kofluyolu Kalp Dergisi Mustafa Saçar MD