Cerebellar cognitive affective syndrome related to chiari malformation: a case report

Abstract

Numerous studies have showed that the cerebellum has a role in processing higher brain functions besides motor coordination. Various types of congenital lesions of cerebellum are associated with neuropsychological impairments and behavioral changes. In Chiari malformation, the cerebellar structures have been stuck in posterior fossa. In this paper a case of Chiari malformation, presenting with affective instability and behavioral disinhibition was described.

Keywords

• cerebellum, affect, behavior, Chiari malformation

Chiari malformasyonuna bağlı serebellar kognitif affektif sendrom: Bir olgu sunumu

Öz

Serebellumun, motor hareketlerin koordinasyonunun yanı sıra, yüksek beyin fonksiyonlarının gerçekleşmesinde rolü olduğu birçok çalışmada gösterilmiştir. Serebellumun konjenital lezyonları çeşitli nöropsikolojik bozukluklar ve davranış değişiklikleri ile ilişkilendirilmiştir. Chiari malformasyonunda, serebellar yapılar posterior fossa içinde sıkışmış halde bulunurlar. Bu yazıda duygusal instabilite ve davranışsal disinhibisyon belirtileri ile giden bir Chiari malformasyonu olgusu sunulmuştur.

Anahtar Kelimeler

• serebellum, afekt, davranış, Chiari malformasyonu

Kaynakça

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