Öksürük Şikayeti ile Gelip Ewing Sarkom Tanısı Alan Hasta

Öz

Ewing sarkomu, dünya çapında en sık görülen ikinci kemik sarkomudur. Tanı anında uzak metastazlara sık rastlanılır, en sık metastaz yeri akciğerlerdir ve en önemli prognostik faktör de tanı anındaki metastatik hastalığın varlığıdır. Ewing sarkomunun prognozu, sistemik kemoterapi ve multimodalite yaklaşımı ile son zamanlarda iyileşmiştir. Biz bu makalede sağ 12. kostadan köken almış ve plevra metastazı sonrası tanı almış olan, kemoterapi tedavisi sonrası yapılan görüntülemelerde kitle tamamen kaybolduğu için cerrahi rezeksiyona gerek duyulmayan bir Ewing Sarkomu olgusunu literatürde ender olarak görülmesi nedeniyle sunmak istedik.

Anahtar Kelimeler

• Çocuk
• Ewing Sarkom
• kitle
• plevral metastaz

Patient Presenting with Cough and Diagnosed as Ewing Sarcoma

Öz

Ewing sarcoma is the second most common bone sarcoma worldwide. Distant metastases are common, with the most frequent site of metastasis being the lungs. The most important prognostic factor is the presence of metastatic disease at the time of diagnosis. The prognosis of Ewing sarcoma has recently improved with systemic chemotherapy and a multimodality approach. In this article, we present a case of Ewing sarcoma originating from the right 12th rib, diagnosed after pleural metastasis. Notably, surgical resection was not required because the mass disappeared completely in imaging studies performed after chemotherapy.

Anahtar Kelimeler

• Child
• Ewing Sarcoma
• mass
• pleural metastasis

Kaynakça

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